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Schema
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Reaction
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Entries
HEXA cleaves the terminal GlcNAc from keratan sulfate
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authored
[InstanceEdit:1630307] Jassal, B, 2011-10-05
catalystActivity
[CatalystActivity:1605773] beta-N-acetylhexosaminidase activity of bHEXA [lysosomal lumen]
category
transition
compartment
[Compartment:161320] lysosomal lumen
created
[InstanceEdit:1638039] Jassal, B, 2011-10-06
dbId
1638053
displayName
HEXA cleaves the terminal GlcNAc from keratan sulfate
edited
[InstanceEdit:1630307] Jassal, B, 2011-10-05
eventOf
[Pathway:R-HSA-2022857] Keratan sulfate degradation - Homo sapiens
input
[SimpleEntity:R-ALL-2105012] GlcNAc-Gal-GlcNAc(S)-Gal [lysosomal lumen]
[SimpleEntity:R-ALL-1605715] H2O [lysosomal lumen]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:1605770] Oligosaccharide structure and amino acid sequence of the major glycopeptides of mature human beta-hexosaminidase
maxDepth
1
modified
[InstanceEdit:10996769] Weiser, Joel, 2026-03-16
name
HEXA cleaves the terminal GlcNAc from keratan sulfate
orthologousEvent
[Reaction:R-DDI-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Dictyostelium discoideum
[Reaction:R-CEL-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Caenorhabditis elegans
[Reaction:R-GGA-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Gallus gallus
[Reaction:R-SSC-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Sus scrofa
[Reaction:R-BTA-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Bos taurus
[Reaction:R-CFA-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Canis familiaris
[Reaction:R-RNO-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Rattus norvegicus
[Reaction:R-MMU-1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - Mus musculus
output
[SimpleEntity:R-ALL-2105010] Gal-GlcNAc(S)-Gal [lysosomal lumen]
[SimpleEntity:R-ALL-1678743] GlcNAc [lysosomal lumen]
precedingEvent
[Reaction:R-HSA-1638032] GNS:Ca2+ cleaves sulfate from GlcNAc-6-sulfate units of keratan sulfate - Homo sapiens
previousReviewStatus
[ReviewStatus:9821385] four stars
releaseDate
2012-06-12
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:2172129] D'Eustachio, P, 2012-03-28
[InstanceEdit:9941989] D'Eustachio, Peter, 2025-03-12
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-1638053
summation
[Summation:1638038] Beta-hexosaminidase (HEX) cleaves the terminal N-acetyl gluc...
updateTrackers
[UpdateTracker:9786960] Update Tracker - [Reaction:1638053] HEXA cleaves the terminal GalNAc from keratan sulfate - v46:[modifyText, removeLiteratureReference]
[UpdateTracker:9953719] Update Tracker - [Reaction:1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - v93:[add_removeOutput, modifyText]
Referrals
(updatedInstance)
[UpdateTracker:9786960] Update Tracker - [Reaction:1638053] HEXA cleaves the terminal GalNAc from keratan sulfate - v46:[modifyText, removeLiteratureReference]
[UpdateTracker:9953719] Update Tracker - [Reaction:1638053] HEXA cleaves the terminal GlcNAc from keratan sulfate - v93:[add_removeOutput, modifyText]
(hasEvent)
[Pathway:R-HSA-2022857] Keratan sulfate degradation
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