paroxysmal nocturnal hemoglobinuria

created [InstanceEdit:9691637] Jassal, Bijay, 2020-06-18
databaseName DOID
dbId 9691636
definition An aquired hemolytic anemia that is characterized by abdominal pain, hematuria, esophageal dysmotility and thrombosis, has_material_basis_in defect in the cell membrane glycosyl phosphatidylinositols that protect red blood cells from the innate complement immune system.
displayName paroxysmal nocturnal hemoglobinuria
identifier 0060284
name
  • paroxysmal nocturnal hemoglobinuria
referenceDatabase [ReferenceDatabase:1247631] DOID
schemaClass Disease
url https://www.ebi.ac.uk/ols4/ontologies/doid/terms?obo_id=DOID:0060284
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