granulomatosis with polyangiitis

created [InstanceEdit:9660848] Orlic-Milacic, Marija, 2019-09-12
databaseName DOID
dbId 9660852
definition An autoimmune hypersensitivity disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels.
displayName granulomatosis with polyangiitis
identifier 12132
name
  • granulomatosis with polyangiitis
referenceDatabase [ReferenceDatabase:1247631] DOID
schemaClass Disease
synonym
  • Wegener granulomatosis, formerly
  • Necrotizing respiratory granulomatosis
url https://www.ebi.ac.uk/ols4/ontologies/doid/terms?obo_id=DOID:12132
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