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dbt [mitochondrial matrix]
Stable Identifier
R-XTR-70017
Type
Protein [EntityWithAccessionedSequence]
Species
Xenopus tropicalis
Compartment
mitochondrial matrix
Synonyms
Lipo-K105-DBT, Q28E15
Locations in the PathwayBrowser
Expand all
Metabolism (Xenopus tropicalis)
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Branched-chain amino acid catabolism (Xenopus tropicalis)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Xenopus tropicalis)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Xenopus tropicalis)
BCKDH [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
DBT transfers BCAA to CoA (Xenopus tropicalis)
BCKDH [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
BCKDH [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
BCKDK phosphorylates BCKDH (Xenopus tropicalis)
BCKDH [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
p-BCKDH [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
Metabolism of proteins (Xenopus tropicalis)
Post-translational protein modification (Xenopus tropicalis)
Protein lipoylation (Xenopus tropicalis)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DBT/DLST (Xenopus tropicalis)
Lipoylated DBT/DLST [mitochondrial matrix] (Xenopus tropicalis)
dbt [mitochondrial matrix] (Xenopus tropicalis)
External Reference Information
External Reference
UniProt:Q28E15
Gene Names
dbt
Reference Genes
BioGPS Gene:549717 dbt
ENSEMBL:ENSXETG00000013210
KEGG:xtr:549717 dbt
Monarch:549717 dbt
NCBI Gene:549717 dbt
UCSC:Q28E15 dbt
Reference Transcript
RefSeq:NM_001016963.2 dbt
Participates
as a member of
Lipoylated DBT/DLST [mitochondrial matrix] (Xenopus tropicalis)
as an input of
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Xenopus tropicalis)
as an output of
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
as a component of
p-BCKDH [mitochondrial matrix] (Xenopus tropicalis)
BCKDH [mitochondrial matrix] (Xenopus tropicalis)
Other forms of this molecule
dbt [cytosol]
dbt [mitochondrial matrix]
dbt [mitochondrial matrix]
dbt [mitochondrial matrix]
dbt [mitochondrial matrix]
dbt [mitochondrial matrix]
Inferred From
Lipo-K105-DBT [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-lipoyl-L-lysine at 105 (in Homo sapiens)
Coordinate
105
PsiMod Name
N6-lipoyl-L-lysine [MOD:00127]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-lipoyl-L-lysine.
Cross References
RefSeq
NP_001016963.1
Xenbase
XB-GENE-965456
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