Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
IDH3A [mitochondrial matrix]
Stable Identifier
R-MMU-70962
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
Q9D6R2
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Citric acid cycle (TCA cycle) (Mus musculus)
IDH3 complex decarboxylates isocitrate (Mus musculus)
IDH3 octamer [mitochondrial matrix] (Mus musculus)
IDH3 complex [mitochondrial matrix] (Mus musculus)
IDH3A [mitochondrial matrix] (Mus musculus)
IDH3A [mitochondrial matrix] (Mus musculus)
Metabolism of proteins (Mus musculus)
Mitochondrial protein degradation (Mus musculus)
CLPXP binds mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
IDH3A [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
IDH3A [mitochondrial matrix] (Mus musculus)
CLPXP degrades mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
IDH3A [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:Q9D6R2
Reference Genes
BioGPS Gene:67834
ENSEMBL:ENSMUSG00000032279
KEGG:mmu:67834
Monarch:67834
NCBI Gene:67834
UCSC:Q9D6R2
Reference Transcript
RefSeq:NM_029573.2
Other Identifiers
10585417
105971_at
1422500_at
1422501_s_at
1432016_a_at
17517390
4330089
4367244
4489156
4493080
4522533
4630219
4722883
4735962
4812598
4838226
4910605
4967668
4990471
5036045
5047217
5190367
5239582
5363190
5394507
5395589
5537534
5614210
67834
94534_at
A_51_P268559
GE39420
GO:0000287
GO:0004449
GO:0005739
GO:0005759
GO:0006099
GO:0006102
GO:0016491
GO:0016616
GO:0043209
GO:0045242
GO:0046872
GO:0051287
ILMN_2740134
aa407078_rc_s_at
mMC009873
Participates
as a member of
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
as a component of
IDH3 complex [mitochondrial matrix] (Mus musculus)
Inferred From
IDH3A [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_083849.1
ENSEMBL
ENSMUST00000167866
,
ENSMUSG00000032279
,
ENSMUSP00000127526
IntEnz
1.1.1.41
PRO
Q9D6R2
GlyGen
Q9D6R2
MGI
1915084
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text