Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
PXLP-AADAT [mitochondrial matrix]
Stable Identifier
R-MMU-70943
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
Q9WVM8
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Lysine catabolism (Mus musculus)
alpha-aminoadipate + alpha-ketoglutarate <=> alpha-ketoadipate + glutamate (Mus musculus)
AADAT dimer [mitochondrial matrix] (Mus musculus)
PXLP-AADAT [mitochondrial matrix] (Mus musculus)
alpha-ketoadipate + glutamate <=> alpha-aminoadipate + alpha-ketoglutarate (Mus musculus)
AADAT dimer [mitochondrial matrix] (Mus musculus)
PXLP-AADAT [mitochondrial matrix] (Mus musculus)
Tryptophan catabolism (Mus musculus)
kynurenine + 2-oxoglutarate => 4-(2-aminophenyl)-2,4-dioxobutanoic acid + glutamate (Mus musculus)
AADAT dimer [mitochondrial matrix] (Mus musculus)
PXLP-AADAT [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:Q9WVM8
Reference Genes
BioGPS Gene:23923
ENSEMBL:ENSMUSG00000057228
KEGG:mmu:23923
Monarch:23923
NCBI Gene:23923
UCSC:Q9WVM8
Reference Transcript
RefSeq:NM_011834.2
Other Identifiers
10571891
115324_at
117219_f_at
117220_r_at
1418519_at
17501329
23923
4413171
4460279
4460888
4483224
4563692
4574323
4683084
4870017
4877383
4901608
4989535
5040370
5051069
5116852
5142863
5195018
5227511
5359694
5386117
5600310
98123_at
A_51_P379618
A_55_P2059820
GE35634
GO:0005739
GO:0005759
GO:0006103
GO:0006520
GO:0006536
GO:0006790
GO:0008483
GO:0009058
GO:0016212
GO:0016740
GO:0030170
GO:0033512
GO:0042803
GO:0047315
GO:0047536
GO:0047958
GO:0050094
GO:0055086
GO:0070189
GO:1901605
ILMN_2594302
mMC004105
Participates
as a component of
AADAT dimer [mitochondrial matrix] (Mus musculus)
Other forms of this molecule
PXLP-AADAT [cytosol]
Inferred From
PXLP-AADAT [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at 263 (in Homo sapiens)
Coordinate
263
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
RefSeq
NP_035964.1
ENSEMBL
ENSMUST00000079472
,
ENSMUSG00000057228
,
ENSMUSP00000078436
IntEnz
2.6.1.39
PRO
Q9WVM8
MGI
1345167
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text