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BCKDHA [mitochondrial matrix]
Stable Identifier
R-MMU-70014
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
P50136
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Branched-chain amino acid catabolism (Mus musculus)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Mus musculus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Mus musculus)
BCKDH [mitochondrial matrix] (Mus musculus)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
DBT transfers BCAA to CoA (Mus musculus)
BCKDH [mitochondrial matrix] (Mus musculus)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
BCKDH [mitochondrial matrix] (Mus musculus)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
BCKDK phosphorylates BCKDH (Mus musculus)
BCKDH [mitochondrial matrix] (Mus musculus)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
p-BCKDH [mitochondrial matrix] (Mus musculus)
BCKDHA:p-BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
PPM1K dephosphorylates p-BCKDH (Mus musculus)
BCKDH [mitochondrial matrix] (Mus musculus)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
p-BCKDH [mitochondrial matrix] (Mus musculus)
BCKDHA:p-BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:P50136
Reference Genes
ENSEMBL:ENSMUSG00000060376
UCSC:P50136
Participates
as a component of
BCKDHA:p-BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Mus musculus)
Inferred From
BCKDHA [mitochondrial matrix]
(Homo sapiens)
Cross References
IntEnz
1.2.4.4
PRO
P50136
MGI
107701
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