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Ndufa2 [mitochondrial inner membrane]
Stable Identifier
R-MMU-60178
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial inner membrane
Synonyms
NDUFA2, Q9CQ75
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Respiratory electron transport (Mus musculus)
Complex I biogenesis (Mus musculus)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Metabolism of proteins (Mus musculus)
Mitochondrial protein degradation (Mus musculus)
LONP1 binds mitochondrial inner membrane proteins (Mus musculus)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Mus musculus)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
LONP1 degrades mitochondrial inner membrane proteins (Mus musculus)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Mus musculus)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Mus musculus)
Ndufa2 [mitochondrial inner membrane] (Mus musculus)
External Reference Information
External Reference
UniProt:Q9CQ75
Gene Names
Ndufa2
Reference Genes
BioGPS Gene:17991 Ndufa2
ENSEMBL:ENSMUSG00000014294
KEGG:mmu:17991 Ndufa2
Monarch:17991 Ndufa2
NCBI Gene:17991 Ndufa2
UCSC:Q9CQ75 Ndufa2
Reference Transcript
RefSeq:NM_010885.5 Ndufa2
Other Identifiers
10458386
1417368_s_at
17353752
17991
5036879
5065199
5174921
5226771
5235093
5451403
96280_at
A_51_P384946
GE119146
GO:0001835
GO:0005739
GO:0005743
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0031966
GO:0042776
GO:0045271
GO:0055085
GO:0055086
GO:1901135
GO:1902600
ILMN_2588601
mMC021470
Participates
as a member of
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Mus musculus)
as a component of
HP subcomplex [mitochondrial inner membrane] (Mus musculus)
Inferred From
NDUFA2 [mitochondrial inner membrane]
(Homo sapiens)
Cross References
RefSeq
NP_035015.2
ENSEMBL
ENSMUSG00000014294
,
ENSMUST00000014438
,
ENSMUSP00000014438
PRO
Q9CQ75
MGI
1343103
PDB
6G2J
,
6ZTQ
,
8UCA
,
8RGP
,
8XNR
,
8XNT
,
8XNS
,
8XNU
,
8IB9
,
8C2S
,
8XNZ
,
7AK5
,
7AK6
,
8IAP
,
8IB4
,
8XNO
,
8IC3
,
8XO0
,
6G72
,
8XNP
,
8IC2
,
8XNV
,
8XNX
,
8XNQ
,
8XNW
,
8XNY
,
8XNN
,
8PW6
,
8CA5
,
8CA3
,
8OLT
,
8XNM
,
8PW5
,
8IBE
,
8XNL
,
8PW7
,
7PSA
,
8IBD
,
8RGQ
,
8RGT
,
8OM1
,
8RGR
,
7B93
,
6ZR2
,
8IAO
,
8IB5
,
8IBA
,
8CA4
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