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OXA1L [mitochondrial matrix]
Stable Identifier
R-HSA-9036893
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Mitochondrial inner membrane protein OXA1L, OXA1L_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Homo sapiens)
Translation (Homo sapiens)
Mitochondrial translation (Homo sapiens)
Mitochondrial translation elongation (Homo sapiens)
55S ribosome with peptidyl-tRNA in A site binds GFM1:GTP (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA at A-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA:GFM1:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
Peptide transfer from P-site to A-site (peptide bond formation) (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA at A-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
TUFM hydrolyzes GTP and TUFM:GDP dissociates from 55S ribosome (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA:TUFM:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
TUFM:GTP:aminoacyl-tRNA binds 55S ribosome:mRNA:fMet-tRNA (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA:TUFM:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
Translocation of peptidyl-tRNA from A-site to P-site (and translocation of 55S ribosome by 3 bases along mRNA) (Homo sapiens)
55S ribosome:mRNA:peptidyl-tRNA at P-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA:GFM1:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
Mitochondrial translation initiation (Homo sapiens)
39S subunit binds 28S subunit:mRNA:fMet-tRNA (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
Mitochondrial translation termination (Homo sapiens)
55S ribosome:MTRF1L hydrolyzes peptidyl-tRNA bond and GTP is hydrolyzed (Homo sapiens)
55S ribosome:mRNA:peptidyl-tRNA:MTRF1L:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
GFM2:GTP binds 55S ribosome:mRNA:tRNA:MRRF releasing mRNA and tRNA (Homo sapiens)
55S ribosome:MRRF:GFM2:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:tRNA:MRRF [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
Hydrolysis of GTP and dissociation of 28S and 39S subunits (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:MRRF:GFM2:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
MRRF binds 55S ribosome:mRNA:tRNA (Homo sapiens)
55S ribosome:mRNA:tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:tRNA:MRRF [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
MTRF1L (MTRF1a) or ICT1 binds stop codon in 55S ribosome:mRNA:peptidyl-tRNA (Homo sapiens)
55S ribosome:mRNA:peptidyl-tRNA at P-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
55S ribosome:mRNA:peptidyl-tRNA:MTRF1L:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
OXA1L [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q15070 OXA1L
Gene Names
OXA1L
Chain
transit peptide:1-, chain:-435
Reference Genes
BioGPS Gene:5018 Q2M1J6
COSMIC (genes):OXA1L OXA1L
CTD Gene:5018 OXA1L
dbSNP Gene:5018 Q2M1J6
ENSEMBL:ENSG00000155463 OXA1L
HGNC:8526 OXA1L
KEGG:hsa:5018 Q2M1J6
Monarch:5018 Q2M1J6
NCBI Gene:5018 Q2M1J6
OMIM:601066 OXA1L
UCSC:Q15070 OXA1L
Reference Transcript
RefSeq:NM_005015.3 Q2M1J6
Other Identifiers
11715497_a_at
11715498_a_at
11747313_a_at
11760867_at
16782153
208717_PM_at
208717_at
3528806
3528807
3528808
3528809
3528810
3528811
3528812
3528813
3528814
3528815
3528816
3528817
3528818
3528819
3528820
3528821
3528822
3528823
3528824
3528825
3528826
3528827
3528828
3528829
3528830
3528831
3528833
3528835
39774_at
5018
7973314
86389_at
A_14_P131304
A_23_P2998
GE60064
GO:0005515
GO:0005739
GO:0005743
GO:0005759
GO:0006091
GO:0007005
GO:0009060
GO:0016020
GO:0031966
GO:0032543
GO:0032780
GO:0032977
GO:0032979
GO:0032981
GO:0032991
GO:0033615
GO:0042803
GO:0043226
GO:0051262
GO:0051354
GO:0061024
GO:0065003
GO:0090150
GO:0097177
GO:0140104
GO:0141164
HMNXSV003022397
ILMN_1731851
PH_hs_0009107
TC14000131.hg
X80695_at
g12804516_3p_at
Participates
as a component of
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
Other forms of this molecule
OXA1L [mitochondrial inner membrane]
Inferred To
Oxa1l [mitochondrial matrix]
(Mus musculus)
Oxa1l [mitochondrial matrix]
(Rattus norvegicus)
OXA1L [mitochondrial matrix]
(Bos taurus)
OXA1L [mitochondrial matrix]
(Canis familiaris)
OXA1L [mitochondrial matrix]
(Drosophila melanogaster)
OXA1L [mitochondrial matrix]
(Sus scrofa)
Ghost homologue of OXA1L [mitochondrial matrix]
(Gallus gallus)
oxa1l [mitochondrial matrix]
(Danio rerio)
oxa-1 [mitochondrial matrix]
(Caenorhabditis elegans)
Cross References
ENSEMBL
ENSP00000483491
,
ENSG00000155463
,
ENST00000612549
,
ENST00000358043
,
ENSP00000350740
OpenTargets
ENSG00000155463
GeneCards
OXA1L
HPA
ENSG00000155463-OXA1L
PRO
Q15070
Pharos - Targets
Q15070
PDB
6ZM5
,
7A5K
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