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PXLP-BCAT2 [mitochondrial matrix]
Stable Identifier
R-HSA-70703
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
branched-chain amino acid aminotransferase, mitochondrial, apoenzyme, BCAT2
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate <=> leu, ile, or val + alpha-ketoglutarate [BCAT2] (Homo sapiens)
BCAT2 dimer [mitochondrial matrix] (Homo sapiens)
PXLP-BCAT2 [mitochondrial matrix] (Homo sapiens)
leu, ile, or val + alpha-ketoglutarate <=> a-ketoisocaproate, a-keto-b-methylvalerate, or a-ketoisovalerate + glutamate [BCAT2] (Homo sapiens)
BCAT2 dimer [mitochondrial matrix] (Homo sapiens)
PXLP-BCAT2 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:O15382 BCAT2
Gene Names
BCAT2, BCATM, BCT2, ECA40
Chain
transit peptide:1-27, chain:28-392
Reference Genes
BioGPS Gene:587 BCAT2
COSMIC (genes):BCAT2 BCAT2
CTD Gene:587 BCAT2
dbSNP Gene:587 BCAT2
ENSEMBL:ENSG00000105552 BCAT2
HGNC:977 BCAT2
KEGG Gene (Homo sapiens):587 BCAT2
Monarch:587 BCAT2
NCBI Gene:587 BCAT2
OMIM:113530 BCAT2
UCSC:O15382 BCAT2
Reference Transcript
RefSeq:NM_001190.3 BCAT2
RefSeq:NM_001164773.1 BCAT2
RefSeq:NM_001284325.1 BCAT2
Other Identifiers
0003390288
11727544_a_at
16874082
203576_PM_at
203576_at
3867419
3867420
3867422
3867423
3867424
3867425
3867428
3867429
3867430
3867433
3867434
41111_at
587
8038202
A_23_P101551
A_23_P90163
GE59360
GO:0003674
GO:0003824
GO:0004084
GO:0005575
GO:0005622
GO:0005634
GO:0005654
GO:0005737
GO:0005739
GO:0005759
GO:0006520
GO:0006549
GO:0006550
GO:0006551
GO:0006573
GO:0006629
GO:0008150
GO:0008483
GO:0008652
GO:0009056
GO:0009058
GO:0009081
GO:0009082
GO:0009083
GO:0009098
GO:0009099
GO:0010817
GO:0016740
GO:0043226
GO:0044281
GO:0050048
GO:0052654
GO:0052655
GO:0052656
GO:1990830
HMNXSV003052812
ILMN_1695110
PH_hs_0026804
TC19001697.hg
TC19002539.hg
U62739_at
g4502374_3p_at
Participates
as a component of
BCAT2 dimer [mitochondrial matrix] (Homo sapiens)
Inferred To
Dmel\CG1673 [mitochondrial matrix]
(Drosophila melanogaster)
BAT1 [mitochondrial matrix]
(Saccharomyces cerevisiae)
BCAT2 [mitochondrial matrix]
(Bos taurus)
BCAT2 [mitochondrial matrix]
(Canis familiaris)
BCAT2 [mitochondrial matrix]
(Sus scrofa)
bcat-1 [mitochondrial matrix]
(Caenorhabditis elegans)
bcaA [mitochondrial matrix]
(Dictyostelium discoideum)
bcat2 [mitochondrial matrix]
(Danio rerio)
bcat2 [mitochondrial matrix]
(Xenopus tropicalis)
eca39 [mitochondrial matrix]
(Schizosaccharomyces pombe)
Bcat2 [mitochondrial matrix]
(Mus musculus)
Bcat2 [mitochondrial matrix]
(Rattus norvegicus)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at 229
Coordinate
229
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
RefSeq
NP_001271254.1
,
NP_001181.2
,
NP_001158245.1
Guide to Pharmacology - Targets
2893
OpenTargets
ENSG00000105552
HPA
ENSG00000105552-BCAT2
GeneCards
O15382
Ensembl
ENSP00000440973
,
ENST00000316273
,
ENST00000545387
,
ENSG00000105552
,
ENSP00000322991
PRO
O15382
Pharos - Targets
O15382
Orphanet
24360
HMDB Protein
HMDBP00516
PDB
5MPR
,
1EKP
,
2A1H
,
5BWR
,
5I5S
,
1EKV
,
5BWT
,
1KT8
,
5BWX
,
5I5U
,
5I5V
,
5I5T
,
5CR5
,
2HDK
,
2HGW
,
5I5W
,
1KTA
,
5BWU
,
5I5X
,
5HNE
,
5I60
,
5I5Y
,
6PRX
,
1EKF
,
2HGX
,
2HHF
,
2HG8
,
5BWV
,
5BWW
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P10809 HSPD1
6
HSPD1(1-573) [cytosol]
(R-HSA-1267989)
HSPD1(1-573) [mitochondrial intermembrane space]
(R-HSA-1267963)
HSPD1(1-26) [mitochondrial matrix]
(R-HSA-8986171)
HSPD1(1-573) [mitochondrial inner membrane]
(R-HSA-1299442)
HSPD1 [mitochondrial inner membrane]
(R-HSA-1299455)
HSPD1 [mitochondrial matrix]
(R-HSA-1299448)
0.536
2
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