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LIAS [mitochondrial matrix]
Stable Identifier
R-HSA-6793627
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
fullName evidence="1"Lipoyl synthase, mitochondrial ecNumber evidence="1"2.8.1.8/ecNumber, LIAS_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Protein lipoylation (Homo sapiens)
LIAS synthesizes lipoyl-GCSH (Homo sapiens)
LIAS:2(4Fe-4S) [mitochondrial matrix] (Homo sapiens)
LIAS [mitochondrial matrix] (Homo sapiens)
LIAS:4Fe-4S [mitochondrial matrix] (Homo sapiens)
LIAS [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:O43766 LIAS
Gene Names
LIAS, LAS, HUSSY-01
Chain
transit peptide:1-27, chain:28-372
Reference Genes
BioGPS Gene:11019 LIAS
COSMIC (genes):LIAS LIAS
CTD Gene:11019 LIAS
dbSNP Gene:11019 LIAS
ENSEMBL:ENSG00000121897 LIAS
HGNC:16429 LIAS
KEGG:hsa:11019 LIAS
Monarch:11019 LIAS
NCBI Gene:11019 LIAS
OMIM:607031 LIAS
UCSC:O43766 LIAS
Reference Transcript
RefSeq:NM_001278592.1 LIAS
RefSeq:NM_194451.3 LIAS
RefSeq:NM_001278590.2 LIAS
RefSeq:NM_001278591.1 LIAS
RefSeq:NM_006859.3 LIAS
Other Identifiers
11019
11718376_s_at
11730301_a_at
11740937_x_at
11754258_a_at
11760515_x_at
11762255_x_at
16966137
16966152
214045_PM_at
214045_at
2724347
2724348
2724349
2724350
2724351
2724352
2724353
2724354
2724355
2724356
2724357
2724358
2724359
2724360
2724361
2724362
2724363
2724364
2724366
2724367
2724368
2724369
2724370
2724371
2724376
2724378
2724379
2724380
2724381
2724382
2724383
2724384
2724385
2724386
2724387
2724388
2724389
2724390
36717_at
70808_r_at
72031_g_at
72033_at
7892797
8094688
8094701
81756_at
A_14_P109179
A_23_P254081
GE55246
GE85759
GO:0001843
GO:0003824
GO:0005739
GO:0005759
GO:0006629
GO:0006790
GO:0006954
GO:0006979
GO:0009107
GO:0016740
GO:0016992
GO:0032496
GO:0043226
GO:0046872
GO:0051536
GO:0051539
HMNXSV003007114
HMNXSV003024229
HMNXSV003033777
HMNXSV003055014
Hs.53531.0.A1_3p_at
ILMN_1736077
ILMN_2393341
TC04000230.hg
TC04000231.hg
TC04001988.hg
Participates
as a component of
LIAS:4Fe-4S [mitochondrial matrix] (Homo sapiens)
LIAS:2(4Fe-4S) [mitochondrial matrix] (Homo sapiens)
Inferred To
Lias [mitochondrial matrix]
(Mus musculus)
Lias [mitochondrial matrix]
(Rattus norvegicus)
LIAS [mitochondrial matrix]
(Bos taurus)
LIAS [mitochondrial matrix]
(Canis familiaris)
LIAS [mitochondrial matrix]
(Gallus gallus)
LIAS [mitochondrial matrix]
(Sus scrofa)
lias-1 [mitochondrial matrix]
(Caenorhabditis elegans)
LIP5 [mitochondrial matrix]
(Saccharomyces cerevisiae)
lipA [mitochondrial matrix]
(Plasmodium falciparum)
lias [mitochondrial matrix]
(Danio rerio)
Las [mitochondrial matrix]
(Drosophila melanogaster)
lip5 [mitochondrial matrix]
(Schizosaccharomyces pombe)
Cross References
RefSeq
NP_001265520.1
,
NP_001265521.1
,
NP_919433.1
,
NP_006850.2
,
NP_001265519.1
ENSEMBL
ENST00000640888
,
ENSP00000340676
,
ENST00000340169
,
ENST00000381846
,
ENSP00000371270
,
ENSG00000121897
,
ENSP00000492260
OpenTargets
ENSG00000121897
IntEnz
2.8.1.8
GeneCards
LIAS
HPA
ENSG00000121897-LIAS
PRO
O43766
Pharos - Targets
O43766
Orphanet
LIAS
HMDB Protein
HMDBP01674
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P23434 GCSH
4
AmMeLipo-K107-GCSH [mitochondrial matrix]
(R-HSA-9930732)
GCSH [mitochondrial matrix]
(R-HSA-5693951)
Lipo-K107-GCSH [mitochondrial matrix]
(R-HSA-6793611)
octanoyl-K107-GCSH [mitochondrial matrix]
(R-HSA-6793586)
0.527
3
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