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DHTKD1 [mitochondrial matrix]
Stable Identifier
R-HSA-6792669
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial ecNumber1.2.4.2/ecNumber, DHTK1_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Lysine catabolism (Homo sapiens)
OADH complex synthesizes glutaryl-CoA from 2-OA (Homo sapiens)
DHTKD1 dimer decarboxylates 2-OA (Homo sapiens)
DHTKD1 dimer [mitochondrial matrix] (Homo sapiens)
DHTKD1:ThDP:Mg2+ [mitochondrial matrix] (Homo sapiens)
DHTKD1 [mitochondrial matrix] (Homo sapiens)
OADH complex [mitochondrial matrix] (Homo sapiens)
DHTKD1 dimer [mitochondrial matrix] (Homo sapiens)
DHTKD1:ThDP:Mg2+ [mitochondrial matrix] (Homo sapiens)
DHTKD1 [mitochondrial matrix] (Homo sapiens)
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
OADH complex [mitochondrial matrix] (Homo sapiens)
DHTKD1 dimer [mitochondrial matrix] (Homo sapiens)
DHTKD1:ThDP:Mg2+ [mitochondrial matrix] (Homo sapiens)
DHTKD1 [mitochondrial matrix] (Homo sapiens)
DLST transfers glutaryl to CoA (Homo sapiens)
OADH complex [mitochondrial matrix] (Homo sapiens)
DHTKD1 dimer [mitochondrial matrix] (Homo sapiens)
DHTKD1:ThDP:Mg2+ [mitochondrial matrix] (Homo sapiens)
DHTKD1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q96HY7 DHTKD1
Gene Names
DHTKD1, KIAA1630
Chain
transit peptide:1-, chain:-919
Reference Genes
BioGPS Gene:55526 DHTKD1
COSMIC (genes):DHTKD1 DHTKD1
CTD Gene:55526 DHTKD1
dbSNP Gene:55526 DHTKD1
ENSEMBL:ENSG00000181192 DHTKD1
HGNC:23537 DHTKD1
KEGG:hsa:55526 DHTKD1
Monarch:55526 DHTKD1
NCBI Gene:55526 DHTKD1
OMIM:614984 DHTKD1
UCSC:Q96HY7 DHTKD1
Reference Transcript
RefSeq:NM_018706.6 DHTKD1
Other Identifiers
11721735_at
11758444_s_at
16702457
209916_3p_at
209916_PM_at
209916_at
227094_PM_at
227094_at
3235374
3235375
3235376
3235381
3235383
3235384
3235387
3235390
3235391
3235392
3235393
3235394
3235395
3235397
3235398
3235399
3235400
3235401
3235402
3235403
3235404
3235405
3235411
3250677
52934_at
55526
7926170
A_14_P107771
A_23_P12601
A_24_P722216
GE61975
GO:0002244
GO:0003824
GO:0004591
GO:0005515
GO:0005739
GO:0005759
GO:0005975
GO:0006091
GO:0006096
GO:0016491
GO:0016624
GO:0030154
GO:0030976
GO:0043226
GO:0055086
GO:0160166
GO:0160167
GO:1901135
HMNXSV003027003
Hs.11732.0.A1_3p_at
ILMN_1664369
PH_hs_0026541
TC10000089.hg
g12803318_3p_x_at
Participates
as a component of
DHTKD1:ThDP:Mg2+ [mitochondrial matrix] (Homo sapiens)
Inferred To
Oadh [mitochondrial matrix]
(Drosophila melanogaster)
dhtkd1 [mitochondrial matrix]
(Danio rerio)
dhtkd1 [mitochondrial matrix]
(Xenopus tropicalis)
ogdh-2 [mitochondrial matrix]
(Caenorhabditis elegans)
odhA [mitochondrial matrix]
(Dictyostelium discoideum)
DHTKD1 [mitochondrial matrix]
(Bos taurus)
DHTKD1 [mitochondrial matrix]
(Canis familiaris)
DHTKD1 [mitochondrial matrix]
(Gallus gallus)
DHTKD1 [mitochondrial matrix]
(Sus scrofa)
Dhtkd1 [mitochondrial matrix]
(Mus musculus)
Dhtkd1 [mitochondrial matrix]
(Rattus norvegicus)
Cross References
ENSEMBL
ENST00000263035
,
ENSP00000263035
,
ENSG00000181192
OpenTargets
ENSG00000181192
GeneCards
DHTKD1
HPA
ENSG00000181192-DHTKD1
PRO
Q96HY7
Pharos - Targets
Q96HY7
Orphanet
DHTKD1
HMDB Protein
HMDBP09099
PDB
5RVY
,
5RVZ
,
5RW0
,
5RW1
,
6U3J
,
5RVW
,
5RVX
,
6SY1
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