Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
PARL [mitochondrial inner membrane]
Stable Identifier
R-HSA-5333637
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Presenilins-associated rhomboid-like protein, mitochondrial ecNumber3.4.21.105/ecNumber, PARL_HUMAN
Locations in the PathwayBrowser
Expand all
Transport of small molecules (Homo sapiens)
Mitochondrial calcium ion transport (Homo sapiens)
Processing of SMDT1 (Homo sapiens)
YME1L1 proteolyzes unassembled proSMDT1 (Homo sapiens)
STOML2:PARL:YME1L [mitochondrial inner membrane] (Homo sapiens)
PARL [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9H300 PARL
Gene Names
PARL, PSARL, PRO2207
Chain
transit peptide:1-52, chain:53-379, peptide:53-77
Reference Genes
BioGPS Gene:55486 PARL
COSMIC - genes:PARL PARL
CTD Gene:55486 PARL
dbSNP Gene:55486 PARL
ENSEMBL:ENSG00000175193 PARL
HGNC:18253 PARL
KEGG:hsa:55486 PARL
Monarch:55486 PARL
NCBI Gene:55486 PARL
OMIM:607858 PARL
UCSC:Q9H300 PARL
Reference Transcript
RefSeq:NM_018622.6 PARL
RefSeq:NM_001037639.3 PARL
Other Identifiers
11731166_a_at
16962112
218271_PM_s_at
218271_s_at
2708231
2708232
2708233
2708234
2708236
2708237
2708238
2708240
2708244
2708245
2708246
2708247
2708252
2708253
2708256
2708258
2708264
2708265
55486
57809_at
8092409
A_24_P221883
A_33_P3335451
GE82427
GE87045
GO:0004175
GO:0004252
GO:0005515
GO:0005634
GO:0005739
GO:0005743
GO:0006465
GO:0006508
GO:0007005
GO:0008053
GO:0008233
GO:0008236
GO:0010821
GO:0016020
GO:0016485
GO:0016787
GO:0030162
GO:0033619
GO:0090201
GO:1901524
GO:1903214
GO:2000377
GO:2001243
HMNXSV003004035
HMNXSV003044582
ILMN_1731354
ILMN_2257665
ILMN_2341467
PH_hs_0001259
PH_hs_0031004
TC03002062.hg
g8924133_3p_s_at
Participates
as a component of
STOML2:PARL:YME1L [mitochondrial inner membrane] (Homo sapiens)
Inferred To
PARL [mitochondrial inner membrane]
(Bos taurus)
PARL [mitochondrial inner membrane]
(Canis familiaris)
PARL [mitochondrial inner membrane]
(Gallus gallus)
Parl [mitochondrial inner membrane]
(Mus musculus)
Parl [mitochondrial inner membrane]
(Rattus norvegicus)
parla [mitochondrial inner membrane]
(Danio rerio)
Cross References
RefSeq
NP_001032728.1
,
NP_061092.3
ENSEMBL
ENSG00000175193
,
ENSP00000310676
,
ENST00000311101
,
ENSP00000325421
,
ENST00000317096
OpenTargets
ENSG00000175193
GeneCards
PARL
HPA
ENSG00000175193-PARL
PRO
Q9H300
Pharos - Targets
Q9H300
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text