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MT-ATP6 [mitochondrial inner membrane]
Stable Identifier
R-HSA-50498
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
ATP synthase A chain , Protein 6
Icon
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Formation of ATP by chemiosmotic coupling (Homo sapiens)
ADP and Pi bind to ATPase (Homo sapiens)
ATPase:ADP:Pi [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
ATPase synthesizes ATP (Homo sapiens)
ATPase:ADP:Pi [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
ATPase:ATP [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
Enzyme-bound ATP is released (Homo sapiens)
ATPase:ATP [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
AFG3L2 binds mitochondrial inner membrane proteins (Homo sapiens)
AFG3L2:substrate protein (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
Substrate of AFG3L2 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
Substrate of AFG3L2 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
AFG3L2 degrades mitochondrial inner membrane proteins (Homo sapiens)
AFG3L2:substrate protein (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
Substrate of AFG3L2 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
Organelle biogenesis and maintenance (Homo sapiens)
Mitochondrial biogenesis (Homo sapiens)
Cristae formation (Homo sapiens)
F1Fo ATP synthase dimerizes (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase dimer [mitochondrial inner membrane] (Homo sapiens)
F1Fo ATP synthase [mitochondrial inner membrane] (Homo sapiens)
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
MT-ATP6 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:P00846 MT-ATP6
Gene Names
MT-ATP6, ATP6, ATPASE6, MTATP6
Chain
chain:1-226
Reference Genes
BioGPS Gene:4508 MT-ATP6
COSMIC (genes):MT-ATP6 MT-ATP6
CTD Gene:4508 MT-ATP6
dbSNP Gene:4508 MT-ATP6
ENSEMBL:ENSG00000198899 MT-ATP6
ENSEMBL_homo_sapiens_GENE:ENSG00000198899.2 MT-ATP6
HGNC:7414 MT-ATP6
KEGG Gene (Homo sapiens):4508 MT-ATP6
Monarch:4508 MT-ATP6
NCBI Gene:4508 MT-ATP6
OMIM:516060 MT-ATP6
Reference Transcript
RefSeq:NC_012920.1 MT-ATP6
Other Identifiers
11758423_s_at
11762922_s_at
11762923_x_at
1553567_3p_s_at
1553567_PM_s_at
1553567_s_at
1553588_PM_at
1553588_at
17100663
17100665
17100667
17100669
17100671
17126266
17126268
17126270
2315317
2315318
2315319
2492706
2492708
4037637
4037639
4037640
4037641
4037642
4037643
4037644
4037645
4037646
4037647
4037648
4037649
4037651
4037653
4037655
4037657
4037658
4037659
4508
7896752
8043375
8165667
8165669
8165672
8165674
A_23_P337726
A_23_P360209
A_33_P3336696
A_33_P3410700
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005753
GO:0006091
GO:0006754
GO:0006811
GO:0015078
GO:0015986
GO:0016020
GO:0016874
GO:0042776
GO:0043226
GO:0045263
GO:0046933
GO:0055085
GO:0055086
GO:0055093
GO:1901135
GO:1902600
HMNXSV003008622
HMNXSV003015713
HMNXSV003022003
HMNXSV003041642
Hs2Affx.1.41.S1_3p_s_at
Hs2Affx.1.52.S1_3p_at
PH_hs_0033947
PH_hs_0036541
RNA143496|tRNA_413_70
TC01000013.hg
TC0M000005.hg
TC0M000006.hg
TC0M000022.hg
Participates
as a member of
Substrate of AFG3L2 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
as a component of
ATPase CF(0) [mitochondrial inner membrane] (Homo sapiens)
Inferred To
MT-ATP6 [mitochondrial inner membrane]
(Bos taurus)
MT-ATP6 [mitochondrial inner membrane]
(Gallus gallus)
MT-ATP6 [mitochondrial inner membrane]
(Sus scrofa)
Mtatp6 [mitochondrial inner membrane]
(Mus musculus)
Mt-atp6 [mitochondrial inner membrane]
(Rattus norvegicus)
atp6 [mitochondrial inner membrane]
(Dictyostelium discoideum)
atp6 [mitochondrial inner membrane]
(Schizosaccharomyces pombe)
mt-atp6 [mitochondrial inner membrane]
(Danio rerio)
mt-atp6 [mitochondrial inner membrane]
(Xenopus tropicalis)
mt:ATPase6 [mitochondrial inner membrane]
(Drosophila melanogaster)
Ghost homologue of MT-ATP6 [mitochondrial inner membrane]
(Canis familiaris)
atp-6 [mitochondrial inner membrane]
(Caenorhabditis elegans)
ATP6 [mitochondrial inner membrane]
(Saccharomyces cerevisiae)
Cross References
RefSeq
YP_003024031.1
Guide to Pharmacology - Targets
801
OpenTargets
ENSG00000198899
HPA
ENSG00000198899-MT-ATP6
GeneCards
P00846
Ensembl
ENST00000361899
,
ENSG00000198899
,
ENSP00000354632
PRO
P00846
Pharos - Targets
P00846
Orphanet
16470
PDB
8H9U
,
8H9S
,
8H9Q
,
8H9J
,
8H9T
,
8H9V
,
8H9M
,
8H9F
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