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FDX1 [mitochondrial matrix]
Stable Identifier
R-HSA-2395500
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Adrenodoxin, mitochondrial, ADX_HUMAN, Ferredoxin 1
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Metabolic disorders of biological oxidation enzymes (Homo sapiens)
Defective CYP11A1 causes AICSR (Homo sapiens)
Defective CYP11A1 does not cleave 20a,22b-DHCHOL (Homo sapiens)
CYP11A1 mutants:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
Metabolism (Homo sapiens)
Biological oxidations (Homo sapiens)
Phase I - Functionalization of compounds (Homo sapiens)
Cytochrome P450 - arranged by substrate type (Homo sapiens)
Endogenous sterols (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX1 (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Metabolism of steroids (Homo sapiens)
Metabolism of steroid hormones (Homo sapiens)
Pregnenolone biosynthesis (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX1 (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
Mitochondrial iron-sulfur cluster biogenesis (Homo sapiens)
Electron transport from NADPH to Ferredoxin (Homo sapiens)
FDXR transfers electrons to FDX1,2 (FDX1L) (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX1 (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Homo sapiens)
FDX1,FDX2 (oxidized) [mitochondrial matrix] (Homo sapiens)
FDX1 (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
FDX1,FDX2 (reduced) [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Protein lipoylation (Homo sapiens)
LIAS synthesizes lipoyl-GCSH (Homo sapiens)
FDX1 (ox.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P10109 FDX1
Gene Names
FDX1, ADX
Chain
transit peptide:1-60, chain:61-184
Reference Genes
BioGPS Gene:2230 FDX1
COSMIC (genes):FDX1 FDX1
CTD Gene:2230 FDX1
dbSNP Gene:2230 FDX1
ENSEMBL:ENSG00000137714 FDX1
ENSEMBL_homo_sapiens_GENE:ENSG00000137714.3 FDX1
HGNC:3638 FDX1
KEGG Gene (Homo sapiens):2230 FDX1
Monarch:2230 FDX1
NCBI Gene:2230 FDX1
OMIM:103260 FDX1
UCSC:P10109 FDX1
Reference Transcript
RefSeq:NM_004109.4 FDX1
Other Identifiers
11724775_at
11758162_s_at
11758335_s_at
16730996
203646_PM_at
203646_at
203647_PM_s_at
203647_s_at
2230
239161_PM_at
239161_at
3348190
3348191
3348192
3348193
3348199
3348203
3348204
3348205
3348206
3348207
3348208
3348209
36893_at
3903445
45831_r_at
7943721
A_23_P357780
A_33_P3343690
GE60507
GO:0003824
GO:0005506
GO:0005739
GO:0005759
GO:0006091
GO:0006629
GO:0006694
GO:0008202
GO:0008203
GO:0009055
GO:0016491
GO:0022900
GO:0042446
GO:0043226
GO:0046872
GO:0051536
GO:0051537
GO:0071320
GO:0140647
GO:1904322
HMNXSV003020877
Hs.27295.0.A1_3p_at
ILMN_2198812
M23668_at
PH_hs_0028687
TC11000988.hg
g13677224_3p_at
g182493_3p_a_at
Participates
as a component of
FDX1 (red.) [mitochondrial matrix] (Homo sapiens)
FDX1 (ox.) [mitochondrial matrix] (Homo sapiens)
Inferred To
FDX1 [mitochondrial matrix]
(Bos taurus)
FDX1 [mitochondrial matrix]
(Canis familiaris)
FDX1 [mitochondrial matrix]
(Danio rerio)
FDX1 [mitochondrial matrix]
(Drosophila melanogaster)
FDX1 [mitochondrial matrix]
(Gallus gallus)
FDX1 [mitochondrial matrix]
(Mus musculus)
FDX1 [mitochondrial matrix]
(Rattus norvegicus)
FDX1 [mitochondrial matrix]
(Sus scrofa)
fdx1 [mitochondrial matrix]
(Xenopus tropicalis)
Cross References
RefSeq
NP_004100.1
OpenTargets
ENSG00000137714
HPA
ENSG00000137714-FDX1
GeneCards
P10109
Ensembl
ENSG00000137714
,
ENST00000260270
,
ENSP00000260270
PRO
P10109
Pharos - Targets
P10109
Orphanet
25184
HMDB Protein
HMDBP02111
PDB
3N9Y
,
3P1M
,
3NA1
,
7M8I
,
3NA0
,
3N9Z
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