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Gal-Xyl-SDC3 [Golgi lumen]
Stable Identifier
R-HSA-2063983
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
Golgi lumen
Synonyms
Syndecan-3, SDC3_HUMAN, SDC3
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective B3GALT6 causes EDSP2 and SEMDJL1 (Homo sapiens)
Defective B3GALT6 does not transfer Gal to the tetrasaccharide linker (Homo sapiens)
Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Gal-Xyl-SDC3 [Golgi lumen] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
A tetrasaccharide linker sequence is required for GAG synthesis (Homo sapiens)
B3GALT6 transfers Gal to the tetrasaccharide linker (Homo sapiens)
Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Gal-Xyl-SDC3 [Golgi lumen] (Homo sapiens)
B4GALT7 transfers Gal group to xylosyl-unit of the tetrasaccharide linker (Homo sapiens)
Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Gal-Xyl-SDC3 [Golgi lumen] (Homo sapiens)
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
A tetrasaccharide linker sequence is required for GAG synthesis (Homo sapiens)
B3GALT6 transfers Gal to the tetrasaccharide linker (Homo sapiens)
Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Gal-Xyl-SDC3 [Golgi lumen] (Homo sapiens)
B4GALT7 transfers Gal group to xylosyl-unit of the tetrasaccharide linker (Homo sapiens)
Gal-Xyl-proteins [Golgi lumen] (Homo sapiens)
Gal-Xyl-SDC3 [Golgi lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75056 SDC3
Gene Names
SDC3, KIAA0468
Chain
chain:1-442
Reference Genes
BioGPS Gene:9672 SDC3
COSMIC (genes):SDC3 SDC3
CTD Gene:9672 SDC3
dbSNP Gene:9672 SDC3
ENSEMBL:ENSG00000162512 SDC3
ENSEMBL_homo_sapiens_GENE:ENSG00000162512 SDC3
HGNC:10660 SDC3
KEGG Gene (Homo sapiens):9672 SDC3
Monarch:9672 SDC3
NCBI Gene:9672 SDC3
OMIM:186357 SDC3
UCSC:O75056 SDC3
Reference Transcript
RefSeq:NM_014654.3 SDC3
Other Identifiers
11739276_at
1554864_a_at
17087
2404219
2404220
2404221
2404227
2404228
2404229
2404230
2404231
2404234
2404248
2404249
25786
48085
9672
A_33_P3241884
AAK39969
AB007937
AF248634
AL445235
BAA32313
BC013974
CAB025786
CCDS30661
D3DPN2
ENSG00000162512
ENSP00000344468
ENST00000339394
EntrezGene:9672
GO:0001523
GO:0002376
GO:0003674
GO:0005515
GO:0005575
GO:0005576
GO:0005622
GO:0005623
GO:0005737
GO:0005764
GO:0005773
GO:0005794
GO:0005796
GO:0005886
GO:0006024
GO:0006027
GO:0006629
GO:0008150
GO:0009056
GO:0009058
GO:0009986
GO:0016020
GO:0016021
GO:0031012
GO:0040011
GO:0042802
GO:0043202
GO:0043226
GO:0048870
GO:0050900
GO:0062023
HGNC:10660
HPA017087
HPA048085
Hs2.158287.2.S1_3p_s_at
ILMN_1663834
ILMN_1802418
IPR001050
IPR003585
IPR027789
IPR030479
IPR031194
MIM:186357
MIM:601665
NM_014654
NP_055469
PF01034
SDC3
SDC3-202
SM00294
TC01002444.hg
uc001bse.3
UPI000045619B
XM_011542463
XM_011542464
XM_011542466
XP_011540765
XP_011540766
XP_011540768
Participant Of
hasMember
Gal-Xyl-proteins [Golgi lumen]
Other forms of this molecule
SDC3 [plasma membrane]
Heparan-SDC3 [Golgi lumen]
Heparan(1)-SDC3 [Golgi lumen]
Heparan(2)-SDC3 [Golgi lumen]
Heparan(3)-SDC3 [Golgi lumen]
Heparan(4)-SDC3 [Golgi lumen]
Gal-Gal-Xyl-SDC3 [Golgi lumen]
GlcA-Gal-Gal-Xyl-SDC3 [Golgi lumen]
XylS-SDC3 [Golgi lumen]
SDC3 [Golgi lumen]
HS(6)-SDC3 [lysosomal lumen]
SDC3 [lysosomal lumen]
HS(6)-SDC3 [plasma membrane]
HS(5)-SDC3 [Golgi lumen]
HS(4)-SDC3 [Golgi lumen]
HS(2)-SDC3 [Golgi lumen]
HS(3)-SDC3 [Golgi lumen]
HS(6)-SDC3 [Golgi lumen]
HS(1)-SDC3 [Golgi lumen]
HS(4)-SDC3 [plasma membrane]
HS(2)-SDC3 [plasma membrane]
HS(1)-SDC3 [plasma membrane]
HS(3)-SDC3 [plasma membrane]
HS(5)-SDC3 [plasma membrane]
Inferred To
Gal-Xyl-SDC3 [Golgi lumen] (Bos taurus)
Gal-Xyl-SDC3 [Golgi lumen] (Caenorhabditis elegans)
Gal-Xyl-SDC3 [Golgi lumen] (Canis familiaris)
Gal-Xyl-SDC3 [Golgi lumen] (Danio rerio)
Gal-Xyl-SDC3 [Golgi lumen] (Drosophila melanogaster)
Gal-Xyl-SDC3 [Golgi lumen] (Gallus gallus)
Gal-Xyl-SDC3 [Golgi lumen] (Mus musculus)
Gal-Xyl-SDC3 [Golgi lumen] (Rattus norvegicus)
Gal-Xyl-SDC3 [Golgi lumen] (Sus scrofa)
Gal-Xyl-SDC3 [Golgi lumen] (Taeniopygia guttata)
Gal-Xyl-SDC3 [Golgi lumen] (Xenopus tropicalis)
Homologues of Gal-Xyl-SDC3 [Golgi lumen] (Sus scrofa)
Homologues of Gal-Xyl-SDC3 [Golgi lumen] (Xenopus tropicalis)
Modified Residues
Name
O-xylosyl-L-serine (ChEBI:63502) at unknown position
Modification
beta-D-Gal-(1->4)-beta-D-Xyl-yl group
PsiMod Name
O-xylosyl-L-serine
PsiMod Definition
A protein modification that effectively converts an L-serine residue to O3-xylosylserine.
Cross References
RefSeq
NP_055469.3
OpenTargets
ENSG00000162512
GeneCards
O75056
PRO
O75056
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