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CYP11A1 [mitochondrial matrix]
Stable Identifier
R-HSA-193148
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Cytochrome P450 11A1
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Biological oxidations (Homo sapiens)
Phase I - Functionalization of compounds (Homo sapiens)
Cytochrome P450 - arranged by substrate type (Homo sapiens)
Endogenous sterols (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (ox.) [mitochondrial matrix] (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Metabolism of steroids (Homo sapiens)
Metabolism of steroid hormones (Homo sapiens)
Pregnenolone biosynthesis (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (ox.) [mitochondrial matrix] (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
CYP11A1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P05108 CYP11A1
Gene Names
CYP11A1, CYP11A
Chain
transit peptide:1-39, chain:40-521
Reference Genes
BioGPS Gene:1583 CYP11A1
COSMIC (genes):CYP11A1 CYP11A1
CTD Gene:1583 CYP11A1
dbSNP Gene:1583 CYP11A1
ENSEMBL:ENSG00000140459 CYP11A1
HGNC:2590 CYP11A1
KEGG:hsa:1583 CYP11A1
Monarch:1583 CYP11A1
NCBI Gene:1583 CYP11A1
OMIM:118485 CYP11A1
UCSC:P05108 CYP11A1
Reference Transcript
RefSeq:NM_000781.3 CYP11A1
RefSeq:NM_001099773.2 CYP11A1
Other Identifiers
11729652_a_at
11750526_a_at
1583
16811617
204309_PM_at
204309_at
3048858
3632863
3632864
3632865
3632866
3632867
3632868
3632869
3632870
3632871
3632872
3632873
3632874
3632875
3632876
3632877
3632878
3632879
3632880
3632881
3632883
3632884
3632885
3632887
3632888
3632889
3632893
3632894
37195_at
3984518
7990333
A_23_P129169
GE57831
GO:0003824
GO:0004497
GO:0005506
GO:0005515
GO:0005739
GO:0005743
GO:0005759
GO:0006629
GO:0006694
GO:0006700
GO:0006704
GO:0006766
GO:0008203
GO:0008207
GO:0008386
GO:0016125
GO:0016491
GO:0016705
GO:0020037
GO:0034650
GO:0042359
GO:0043226
GO:0044281
GO:0046872
GO:0071375
HMNXSV003007473
ILMN_1768820
M14565_at
PH_hs_0004396
TC15001642.hg
TC15002624.hg
g4503188_3p_at
Participates
as a component of
CYP11A1:FDXR:FDX1,FDX1L (ox.) [mitochondrial matrix] (Homo sapiens)
CYP11A1:FDXR:FDX1,FDX1L (red.) [mitochondrial matrix] (Homo sapiens)
Other forms of this molecule
CYP11A1 D271_V272insGD [mitochondrial matrix]
CYP11A1 V415E [mitochondrial matrix]
CYP11A1 I279Yfs*10 [mitochondrial matrix]
Inferred To
cyp11a1.1 [mitochondrial matrix]
(Danio rerio)
CYP11A1 [mitochondrial matrix]
(Bos taurus)
CYP11A1 [mitochondrial matrix]
(Canis familiaris)
CYP11A1 [mitochondrial matrix]
(Gallus gallus)
CYP11A1 [mitochondrial matrix]
(Sus scrofa)
Cyp11a1 [mitochondrial matrix]
(Mus musculus)
Cyp11a1 [mitochondrial matrix]
(Rattus norvegicus)
cyp11a1 [mitochondrial matrix]
(Xenopus tropicalis)
Cross References
RefSeq
NP_001093243.1
,
NP_000772.2
Guide to Pharmacology - Targets
1358
OpenTargets
ENSG00000140459
ENSEMBL
ENSP00000500767
,
ENST00000672385
,
ENSP00000268053
,
ENSP00000499849
,
ENST00000672913
,
ENSP00000351455
,
ENST00000268053
,
ENSG00000140459
,
ENST00000358632
,
ENSG00000288362
ZINC - Substances
CP11A_HUMAN
ZINC target
P05108
PRO
P05108
PDB
3NA1
,
3N9Z
,
3NA0
,
3N9Y
IntEnz
1.14.15.6
HPA
ENSG00000140459-CYP11A1
GeneCards
CYP11A1
Pharos - Targets
P05108
ZINC - Predictions - Purchasable
CP11A_HUMAN
Orphanet
CYP11A1
HMDB Protein
HMDBP00724
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