Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
ALDH6A1 [mitochondrial matrix]
Stable Identifier
R-CFA-70890
Type
Protein [EntityWithAccessionedSequence]
Species
Canis familiaris
Compartment
mitochondrial matrix
Synonyms
ALDH6A1, A0A8I3NRV2
Locations in the PathwayBrowser
Expand all
Metabolism (Canis familiaris)
Metabolism of amino acids and derivatives (Canis familiaris)
Branched-chain amino acid catabolism (Canis familiaris)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Canis familiaris)
ALDH6A1 [mitochondrial matrix] (Canis familiaris)
External Reference Information
External Reference
UniProt:A0A8I3NRV2
Gene Names
ALDH6A1
Reference Genes
BioGPS Gene:490779 ALDH6A1
ENSEMBL:ENSCAFG00845013992.1
KEGG:cfa:490779 ALDH6A1
Monarch:490779 ALDH6A1
NCBI Gene:490779 ALDH6A1
UCSC:A0A8I3NRV2 ALDH6A1
Reference Transcript
RefSeq:XM_038545249.1 ALDH6A1
RefSeq:XM_005623655.4 ALDH6A1
RefSeq:XM_038674171.1 ALDH6A1
Other Identifiers
490779
Cfa.17976.1.S1_s_at
CfaAffx.25842.1.S1_at
GO:0004491
GO:0005654
GO:0005739
GO:0006210
GO:0006520
GO:0006574
GO:0016491
GO:0016620
GO:0030154
GO:0050873
GO:0055086
Inferred From
ALDH6A1 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
XP_038530099.1
,
XP_005623712.1
,
XP_038401177.1
ENSEMBL
ENSCAFT00845025031
,
ENSCAFP00845019691
,
ENSCAFG00845013992
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text