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BCKDHA [mitochondrial matrix]
Stable Identifier
R-CEL-70014
Type
Protein [EntityWithAccessionedSequence]
Species
Caenorhabditis elegans
Compartment
mitochondrial matrix
Synonyms
O45924
Locations in the PathwayBrowser
Expand all
Metabolism (Caenorhabditis elegans)
Metabolism of amino acids and derivatives (Caenorhabditis elegans)
Branched-chain amino acid catabolism (Caenorhabditis elegans)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Caenorhabditis elegans)
BCKDH [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA [mitochondrial matrix] (Caenorhabditis elegans)
DBT transfers BCAA to CoA (Caenorhabditis elegans)
BCKDH [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA [mitochondrial matrix] (Caenorhabditis elegans)
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
BCKDH [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA [mitochondrial matrix] (Caenorhabditis elegans)
External Reference Information
External Reference
UniProt:O45924
Reference Genes
BioGPS Gene:176716
ENSEMBL:WBGene00012713
KEGG:cel:CELE_Y39E4A.3
Monarch:176716
NCBI Gene:176716
UCSC:O45924
Wormbase:WBGene00012713
Wormbase:WBGene00012713
Reference Transcript
RefSeq:NM_001038287.6
Other Identifiers
176716
GO:0003863
GO:0005739
GO:0005759
GO:0006520
GO:0006629
GO:0006631
GO:0006633
GO:0009083
GO:0016491
GO:0016624
GO:0046872
GO:0160157
Participates
as a component of
BCKDHA:p-BCKDHB tetramer [mitochondrial matrix] (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer [mitochondrial matrix] (Caenorhabditis elegans)
Inferred From
BCKDHA [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_001033376.1
ENSEMBL
Y39E4A.3a.2
,
Y39E4A.3a.1
,
WBGene00012713
,
Y39E4A.3a.1
,
Y39E4A.3a.2
PRO
O45924
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