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AdoCbl [mitochondrial matrix]
Stable Identifier
R-ALL-3159297
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Synonyms
adenosylcobalamin, cobamamide
Locations in the PathwayBrowser for interactor UniProt:P22033 MMUT
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of vitamins and cofactors (Bos taurus)
Metabolism of water-soluble vitamins and cofactors (Bos taurus)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Bos taurus)
Cobalamin (Cbl) metabolism (Bos taurus)
MMAA:MUT binds AdoCbl (Bos taurus)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Bos taurus)
AdoCbl [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Metabolism of vitamins and cofactors (Caenorhabditis elegans)
Metabolism of water-soluble vitamins and cofactors (Caenorhabditis elegans)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Caenorhabditis elegans)
Cobalamin (Cbl) metabolism (Caenorhabditis elegans)
MMAA:MUT binds AdoCbl (Caenorhabditis elegans)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Caenorhabditis elegans)
AdoCbl [mitochondrial matrix]
Metabolism (Canis familiaris)
Metabolism of vitamins and cofactors (Canis familiaris)
Metabolism of water-soluble vitamins and cofactors (Canis familiaris)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Canis familiaris)
Cobalamin (Cbl) metabolism (Canis familiaris)
MMAA:MUT binds AdoCbl (Canis familiaris)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Canis familiaris)
AdoCbl [mitochondrial matrix]
Metabolism (Danio rerio)
Metabolism of vitamins and cofactors (Danio rerio)
Metabolism of water-soluble vitamins and cofactors (Danio rerio)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Danio rerio)
Cobalamin (Cbl) metabolism (Danio rerio)
MMAA:MUT binds AdoCbl (Danio rerio)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Danio rerio)
AdoCbl [mitochondrial matrix]
Metabolism (Dictyostelium discoideum)
Metabolism of vitamins and cofactors (Dictyostelium discoideum)
Metabolism of water-soluble vitamins and cofactors (Dictyostelium discoideum)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Dictyostelium discoideum)
Cobalamin (Cbl) metabolism (Dictyostelium discoideum)
MMAB adenosylates cob(I)alamin (Dictyostelium discoideum)
AdoCbl [mitochondrial matrix]
Metabolism (Gallus gallus)
Metabolism of vitamins and cofactors (Gallus gallus)
Metabolism of water-soluble vitamins and cofactors (Gallus gallus)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Gallus gallus)
Cobalamin (Cbl) metabolism (Gallus gallus)
MMAA:MUT binds AdoCbl (Gallus gallus)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Gallus gallus)
AdoCbl [mitochondrial matrix]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Defects in vitamin and cofactor metabolism (Homo sapiens)
Defects in cobalamin (B12) metabolism (Homo sapiens)
Defective MMAA causes MMA, cblA type (Homo sapiens)
Defective MMAA does not protect MUT (Homo sapiens)
AdoCbl [mitochondrial matrix]
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of water-soluble vitamins and cofactors (Homo sapiens)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Homo sapiens)
Cobalamin (Cbl) metabolism (Homo sapiens)
MMAA:MUT binds AdoCbl (Homo sapiens)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Homo sapiens)
AdoCbl [mitochondrial matrix]
Metabolism (Mus musculus)
Metabolism of vitamins and cofactors (Mus musculus)
Metabolism of water-soluble vitamins and cofactors (Mus musculus)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Mus musculus)
Cobalamin (Cbl) metabolism (Mus musculus)
MMAA:MUT binds AdoCbl (Mus musculus)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Mus musculus)
AdoCbl [mitochondrial matrix]
Metabolism (Rattus norvegicus)
Metabolism of vitamins and cofactors (Rattus norvegicus)
Metabolism of water-soluble vitamins and cofactors (Rattus norvegicus)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Rattus norvegicus)
Cobalamin (Cbl) metabolism (Rattus norvegicus)
MMAA:MUT binds AdoCbl (Rattus norvegicus)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Rattus norvegicus)
AdoCbl [mitochondrial matrix]
Metabolism (Sus scrofa)
Metabolism of vitamins and cofactors (Sus scrofa)
Metabolism of water-soluble vitamins and cofactors (Sus scrofa)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Sus scrofa)
Cobalamin (Cbl) metabolism (Sus scrofa)
MMAA:MUT binds AdoCbl (Sus scrofa)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Sus scrofa)
AdoCbl [mitochondrial matrix]
Metabolism (Xenopus tropicalis)
Metabolism of vitamins and cofactors (Xenopus tropicalis)
Metabolism of water-soluble vitamins and cofactors (Xenopus tropicalis)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Xenopus tropicalis)
Cobalamin (Cbl) metabolism (Xenopus tropicalis)
MMAA:MUT binds AdoCbl (Xenopus tropicalis)
AdoCbl [mitochondrial matrix]
MMAB adenosylates cob(I)alamin (Xenopus tropicalis)
AdoCbl [mitochondrial matrix]
External Reference Information
External Reference
cobamamide [ChEBI:18408]
Participates
as a component of
mutant MUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Sus scrofa)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Xenopus tropicalis)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Danio rerio)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Caenorhabditis elegans)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Bos taurus)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Rattus norvegicus)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Mus musculus)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Gallus gallus)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Canis familiaris)
2xMMAA:2xMUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
2xMUT:AdoCbl [mitochondrial matrix] (Danio rerio)
2xMUT:AdoCbl [mitochondrial matrix] (Sus scrofa)
2xMUT:AdoCbl [mitochondrial matrix] (Xenopus tropicalis)
2xMUT:AdoCbl [mitochondrial matrix] (Rattus norvegicus)
2xMUT:AdoCbl [mitochondrial matrix] (Bos taurus)
2xMUT:AdoCbl [mitochondrial matrix] (Caenorhabditis elegans)
2xMUT:AdoCbl [mitochondrial matrix] (Gallus gallus)
2xMUT:AdoCbl [mitochondrial matrix] (Mus musculus)
2xMUT:AdoCbl [mitochondrial matrix] (Canis familiaris)
2xMUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
as an input of
Defective MMAA does not protect MUT (Homo sapiens)
MMAA:MUT binds AdoCbl (Caenorhabditis elegans)
MMAA:MUT binds AdoCbl (Gallus gallus)
MMAA:MUT binds AdoCbl (Xenopus tropicalis)
MMAA:MUT binds AdoCbl (Danio rerio)
MMAA:MUT binds AdoCbl (Sus scrofa)
MMAA:MUT binds AdoCbl (Bos taurus)
MMAA:MUT binds AdoCbl (Canis familiaris)
MMAA:MUT binds AdoCbl (Rattus norvegicus)
MMAA:MUT binds AdoCbl (Mus musculus)
MMAA:MUT binds AdoCbl (Homo sapiens)
as an output of
MMAB adenosylates cob(I)alamin (Dictyostelium discoideum)
MMAB adenosylates cob(I)alamin (Caenorhabditis elegans)
MMAB adenosylates cob(I)alamin (Gallus gallus)
MMAB adenosylates cob(I)alamin (Xenopus tropicalis)
MMAB adenosylates cob(I)alamin (Danio rerio)
MMAB adenosylates cob(I)alamin (Sus scrofa)
MMAB adenosylates cob(I)alamin (Bos taurus)
MMAB adenosylates cob(I)alamin (Canis familiaris)
MMAB adenosylates cob(I)alamin (Rattus norvegicus)
MMAB adenosylates cob(I)alamin (Mus musculus)
MMAB adenosylates cob(I)alamin (Homo sapiens)
Cross References
COMPOUND
C00194
PubChem Substance
8143774
HMDB Metabolite
HMDB0002086
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