R-HSA-3296469_v80AdoCblCblSuccinyl-CoAL-MM-CoAMeCblB12rB12rB12sCblCblTCN2DIETTARGET CELLENDOSOMEENTEROCYTEMITOCHONDRIONLYSOSOMEABCD4ABCC1LYSOSOMEdegradationreductionCOFACTORCOFACTORMTRRDEFECTIVE MTRR CAUSES HMAEXXX/YYYCblCblCBLIFCBLIFDEFECTIVE CBLIF CAUSES IFDXXX/YYYAMNDEFECTIVE AMN CAUSES MGA1XXX/YYYCUBNDEFECTIVE CUBN CAUSES MGA1XXX/YYYDEFECTIVE ABCD4 CAUSES MAHCJXXX/YYYMMACHCDEFECTIVE MMACHC CAUSES MAHCCXXX/YYYMMADHCDEFECTIVE MMADHC CAUSES MMAHCDXXX/YYYMTRDEFECTIVE MTR CAUSES HMAGXXX/YYYMMABDEFECTIVE MMAB CAUSES MMA, CBLB TYPEXXX/YYYMMAADEFECTIVE MMAA CAUSES MMA, CBLA TYPEXXX/YYYCblCD320DEFECTIVE CD320 CAUSES MMATCXXX/YYYCblTCN2DEFECTIVE TCN2 CAUSES TCN2 DEFICIENCYXXX/YYY