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Schema
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Reaction
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Entries
ALDH5A1 dehydrogenates SUCCSA to SUCCA
Show undefined attributes
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authored
[InstanceEdit:888551] Mahajan, SS, 2010-06-29
catalystActivity
[CatalystActivity:916830] succinate-semialdehyde dehydrogenase (NAD+) activity of ALDH5A1 tetramer [mitochondrial matrix]
catalystActivityReference
[CatalystActivityReference:9653548] succinate-semialdehyde dehydrogenase (NAD+) activity of ALDH5A1 tetramer [mitochondrial matrix] Redox-switch modulation of human SSADH by dynamic catalytic loop
category
transition
compartment
[Compartment:5460] mitochondrial matrix
created
[InstanceEdit:888547] Mahajan, SS, 2010-06-29
crossReference
[DatabaseIdentifier:11880389] Rhea:13218
dbId
888548
displayName
ALDH5A1 dehydrogenates SUCCSA to SUCCA
edited
[InstanceEdit:918259] Mahajan, SS, 2010-08-03
eventOf
[Pathway:R-HSA-916853] Degradation of GABA - Homo sapiens
followingEvent
[Reaction:R-HSA-70994] SDH complex dehydrogenates succinate - Homo sapiens
input
[SimpleEntity:R-ALL-113521] H2O [mitochondrial matrix]
[SimpleEntity:R-ALL-113526] NAD+ [mitochondrial matrix]
[SimpleEntity:R-ALL-880046] SUCCSA [mitochondrial matrix]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:9653544] Two exon-skipping mutations as the molecular basis of succinic semialdehyde dehydrogenase deficiency (4-hydroxybutyric aciduria)
[LiteratureReference:916840] Redox-switch modulation of human SSADH by dynamic catalytic loop
modified
[InstanceEdit:11879863] Wright, Adam, 2024-03-11
name
ALDH5A1 dehydrogenates SUCCSA to SUCCA
Conversion of succinate semialdehyde to succinate
orthologousEvent
[Reaction:R-MMU-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Mus musculus
[Reaction:R-SCE-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Saccharomyces cerevisiae
[Reaction:R-SPO-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Schizosaccharomyces pombe
[Reaction:R-CEL-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Caenorhabditis elegans
[Reaction:R-DME-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Drosophila melanogaster
[Reaction:R-GGA-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Gallus gallus
[Reaction:R-XTR-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Xenopus tropicalis
[Reaction:R-SSC-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Sus scrofa
[Reaction:R-BTA-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Bos taurus
[Reaction:R-CFA-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Canis familiaris
[Reaction:R-RNO-888548] ALDH5A1 dehydrogenates SUCCSA to SUCCA - Rattus norvegicus
output
2 ×
[SimpleEntity:R-ALL-113529] H+ [mitochondrial matrix]
[SimpleEntity:R-ALL-29362] NADH [mitochondrial matrix]
[SimpleEntity:R-ALL-113536] SUCCA [mitochondrial matrix]
precedingEvent
[Reaction:R-HSA-916855] PXLP-K357-ABAT dimer:2Fe-2S transforms GABA to SUCCSA - Homo sapiens
releaseDate
2010-09-21
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:386898] Restituito, S, 2008-11-27 12:38:49
[InstanceEdit:9653791] Jassal, Bijay, 2019-07-15
revised
[InstanceEdit:9653175] D'Eustachio, Peter, 2019-07-10
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-888548
summation
[Summation:916834] Mitochondrial succinate semialdehyde dehydrogenase (ALDH5A1)...
Referrals
(hasEvent)
[Pathway:R-HSA-916853] Degradation of GABA
(precedingEvent)
[Reaction:R-HSA-70994] SDH complex dehydrogenates succinate
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