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Schema
>
Reaction
>
Entries
limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin
Show undefined attributes
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catalystActivity
[CatalystActivity:71550] 4-alpha-glucanotransferase activity of AGL [cytosol]
catalystActivityReference
[CatalystActivityReference:9643183] 4-alpha-glucanotransferase activity of AGL [cytosol] Glycogen debranching enzyme: purification, antibody characterization, and immunoblot analyses of type III glycogen storage disease.
category
transition
compartment
[Compartment:70101] cytosol
dbId
71552
displayName
limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin
eventOf
[Pathway:R-HSA-70221] Glycogen breakdown (glycogenolysis) - Homo sapiens
followingEvent
[Reaction:R-HSA-71593] ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl)glycogenin => poly{(1,4)-alpha-glucosyl} glycogenin + alpha-D-glucose - Homo sapiens
input
[DefinedSet:R-HSA-453336] limit dextrin-glycogenin dimer [cytosol]
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:71546] Glycogen debranching enzyme: purification, antibody characterization, and immunoblot analyses of type III glycogen storage disease.
[LiteratureReference:70230] Mutations in exon 3 of the glycogen debranching enzyme gene are associated with glycogen storage disease type III that is differentially expressed in liver and muscle.
modified
[InstanceEdit:10901498] Wright, Adam, 2024-03-08
name
limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin
orthologousEvent
[Reaction:R-SCE-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Saccharomyces cerevisiae
[Reaction:R-DDI-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Dictyostelium discoideum
[Reaction:R-CEL-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Caenorhabditis elegans
[Reaction:R-DME-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Drosophila melanogaster
[Reaction:R-GGA-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Gallus gallus
[Reaction:R-XTR-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Xenopus tropicalis
[Reaction:R-SSC-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Sus scrofa
[Reaction:R-BTA-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Bos taurus
[Reaction:R-CFA-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Canis familiaris
[Reaction:R-RNO-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Rattus norvegicus
[Reaction:R-MMU-71552] limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin - Mus musculus
output
[DefinedSet:R-HSA-453350] ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl)GYG dimer [cytosol]
precedingEvent
[Reaction:R-HSA-71515] glycogen-glycogenin-1 + n orthophosphate => limit dextrin-glycogenin-1 + n D-glucose 1-phosphate [PYGM,PYGB] - Homo sapiens
[Reaction:R-HSA-71590] glycogen-glycogenin-2 + n orthophosphate => limit dextrin-glycogenin-2 + n D-glucose 1-phosphate [PYGL] - Homo sapiens
releaseDate
2004-07-06
reviewStatus
[ReviewStatus:9821382] five stars
revised
[InstanceEdit:453329] D'Eustachio, P, 2010-01-21
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-71552
summation
[Summation:178933] Cytosolic debranching enzyme associated with glycogen granul...
Referrals
(hasEvent)
[Pathway:R-HSA-70221] Glycogen breakdown (glycogenolysis)
(precedingEvent)
[Reaction:R-HSA-71593] ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl)glycogenin => poly{(1,4)-alpha-glucosyl} glycogenin + alpha-D-glucose
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