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Schema
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Reaction
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Entries
HGSNAT oligomer acetylates Heparan chain(1)
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authored
[InstanceEdit:2090024] Jassal, B, 2012-02-06
catalystActivity
[CatalystActivity:1678732] heparan-alpha-glucosaminide N-acetyltransferase activity of HGSNAT oligomer [lysosomal membrane]
category
transition
compartment
[Compartment:17938] lysosomal membrane
[Compartment:70101] cytosol
[Compartment:161320] lysosomal lumen
created
[InstanceEdit:2090024] Jassal, B, 2012-02-06
dbId
2090085
displayName
HGSNAT oligomer acetylates Heparan chain(1)
edited
[InstanceEdit:2090024] Jassal, B, 2012-02-06
eventOf
[Pathway:R-HSA-2024096] HS-GAG degradation - Homo sapiens
followingEvent
[Reaction:R-HSA-2090038] NAGLU hydrolyses heparan chain(2) - Homo sapiens
input
[SimpleEntity:R-ALL-76183] Ac-CoA [cytosol]
[SimpleEntity:R-ALL-2090045] Heparan chain(1) [lysosomal lumen]
isChimeric
false
isInDisease
false
isInferred
false
literatureReference
[LiteratureReference:1678735] Analysis of the biogenesis of heparan sulfate acetyl-CoA:alpha-glucosaminide N-acetyltransferase provides insights into the mechanism underlying its complete deficiency in mucopolysaccharidosis IIIC
[LiteratureReference:1678726] Identification of the gene encoding the enzyme deficient in mucopolysaccharidosis IIIC (Sanfilippo disease type C)
[LiteratureReference:1678723] Mutations in TMEM76* cause mucopolysaccharidosis IIIC (Sanfilippo C syndrome)
modified
[InstanceEdit:10818988] Wright, Adam, 2024-03-08
name
HGSNAT oligomer acetylates Heparan chain(1)
orthologousEvent
[Reaction:R-DDI-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Dictyostelium discoideum
[Reaction:R-DME-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Drosophila melanogaster
[Reaction:R-GGA-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Gallus gallus
[Reaction:R-XTR-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Xenopus tropicalis
[Reaction:R-SSC-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Sus scrofa
[Reaction:R-BTA-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Bos taurus
[Reaction:R-CFA-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Canis familiaris
[Reaction:R-RNO-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Rattus norvegicus
[Reaction:R-MMU-2090085] HGSNAT oligomer acetylates Heparan chain(1) - Mus musculus
output
[SimpleEntity:R-ALL-76194] CoA-SH [cytosol]
[SimpleEntity:R-ALL-2090053] Heparan chain(2) [lysosomal lumen]
precedingEvent
[Reaction:R-HSA-2090043] SGSH hydrolyses Heparan sulfate chain(7) - Homo sapiens
releaseDate
2012-06-12
reviewStatus
[ReviewStatus:9821382] five stars
reviewed
[InstanceEdit:2172129] D'Eustachio, P, 2012-03-28
schemaClass
Reaction
species
[Species:48887] Homo sapiens
stId
R-HSA-2090085
summation
[Summation:2457607] Heparan-alpha-glucosaminide N-acetyltransferase (HGSNAT) ace...
Referrals
(normalReaction)
[FailedReaction:R-HSA-2263492] Defective HGSNAT does not acetylate Heparan chain(1)
(hasEvent)
[Pathway:R-HSA-2024096] HS-GAG degradation
(precedingEvent)
[Reaction:R-HSA-2090038] NAGLU hydrolyses heparan chain(2)
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