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gcsh [mitochondrial matrix]
Stable Identifier
R-XTR-6793611
Type
Protein [EntityWithAccessionedSequence]
Species
Xenopus tropicalis
Compartment
mitochondrial matrix
Synonyms
Lipo-K107-GCSH, Q63ZZ2
Locations in the PathwayBrowser
Expand all
Metabolism (Xenopus tropicalis)
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Glyoxylate metabolism and glycine degradation (Xenopus tropicalis)
Glycine degradation (Xenopus tropicalis)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Xenopus tropicalis)
gcsh [mitochondrial matrix] (Xenopus tropicalis)
Metabolism of proteins (Xenopus tropicalis)
Post-translational protein modification (Xenopus tropicalis)
Protein lipoylation (Xenopus tropicalis)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DBT/DLST (Xenopus tropicalis)
gcsh [mitochondrial matrix] (Xenopus tropicalis)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DLAT (Xenopus tropicalis)
gcsh [mitochondrial matrix] (Xenopus tropicalis)
External Reference Information
External Reference
UniProt:Q63ZZ2
Gene Names
gcsh
Reference Genes
BioGPS Gene:496433 gcsh
ENSEMBL:ENSXETG00000047032
KEGG Gene (Xenopus tropicalis):496433 gcsh
Monarch:496433 gcsh
NCBI Gene:496433 gcsh
Reference Transcript
RefSeq:NM_001011024.1 gcsh
Other Identifiers
496433
GO:0005739
GO:0005960
GO:0006520
GO:0019464
GO:0043226
Participates
as an output of
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Xenopus tropicalis)
as an input of
LIPT1 transfers lipoyl group from lipoyl-GCSH to DLAT (Xenopus tropicalis)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DBT/DLST (Xenopus tropicalis)
Other forms of this molecule
gcsh [mitochondrial matrix]
gcsh [mitochondrial matrix]
Inferred From
Lipo-K107-GCSH [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-lipoyl-L-lysine at 107 (in Homo sapiens)
Coordinate
107
PsiMod Name
N6-lipoyl-L-lysine [MOD:00127]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-lipoyl-L-lysine.
Cross References
RefSeq
NP_001011024.1
Xenbase
XB-GENE-956061
Ensembl
ENSXETP00000104270
,
ENSXETT00000108841
,
ENSXETG00000047032
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