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FH [mitochondrial matrix]
Stable Identifier
R-SSC-70980
Type
Protein [EntityWithAccessionedSequence]
Species
Sus scrofa
Compartment
mitochondrial matrix
Synonyms
P10173
Locations in the PathwayBrowser
Expand all
Metabolism (Sus scrofa)
Aerobic respiration and respiratory electron transport (Sus scrofa)
Citric acid cycle (TCA cycle) (Sus scrofa)
FH tetramer hydrates fumarate to L-malate (Sus scrofa)
FH tetramer [mitochondrial matrix] (Sus scrofa)
FH [mitochondrial matrix] (Sus scrofa)
Metabolism of proteins (Sus scrofa)
Mitochondrial protein degradation (Sus scrofa)
CLPXP binds mitochondrial matrix proteins (Sus scrofa)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
FH [mitochondrial matrix] (Sus scrofa)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
FH [mitochondrial matrix] (Sus scrofa)
CLPXP degrades mitochondrial matrix proteins (Sus scrofa)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
FH [mitochondrial matrix] (Sus scrofa)
LONP1 binds mitochondrial matrix proteins (Sus scrofa)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
FH [mitochondrial matrix] (Sus scrofa)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
FH [mitochondrial matrix] (Sus scrofa)
LONP1 degrades mitochondrial matrix proteins (Sus scrofa)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
FH [mitochondrial matrix] (Sus scrofa)
External Reference Information
External Reference
UniProt:P10173
Reference Genes
BioGPS Gene:100627128
ENSEMBL:ENSSSCG00000028178
ENSEMBL:ENSSSCG00000028178.4
ENSEMBL:ENSSSCG00030028801.1
ENSEMBL:ENSSSCG00065076536.1
KEGG Gene (Sus scrofa):100627128
Monarch:100627128
NCBI Gene:100627128
Reference Transcript
RefSeq:NM_001243588.1
Other Identifiers
100627128
GO:0003824
GO:0004333
GO:0005739
GO:0005759
GO:0006091
GO:0006099
GO:0006106
GO:0006108
GO:0016829
GO:0043226
GO:0045239
GO:0048873
GO:0120162
Ssc.17292.1.S1_at
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
as a component of
FH tetramer [mitochondrial matrix] (Sus scrofa)
Inferred From
FH [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_001230517.1
Ensembl
ENSSSCG00000028178
,
ENSSSCP00000026068
,
ENSSSCT00000030683
ZINC target
P10173
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