Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
NDUFS3 [mitochondrial matrix]
Stable Identifier
R-SSC-163927
Type
Protein [EntityWithAccessionedSequence]
Species
Sus scrofa
Compartment
mitochondrial matrix
Synonyms
NDUFS3, A0A286ZNN4
Locations in the PathwayBrowser
Expand all
Metabolism (Sus scrofa)
Aerobic respiration and respiratory electron transport (Sus scrofa)
Respiratory electron transport (Sus scrofa)
Complex I biogenesis (Sus scrofa)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Sus scrofa)
315kDa subcomplex [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Intermediate 2 [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
NDUF subunits bind to form the IP subcomplex (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Sus scrofa)
815kDa complex [mitochondrial inner membrane] (Sus scrofa)
550kDa complex [mitochondrial inner membrane] (Sus scrofa)
315kDa subcomplex [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
980kDa complex [mitochondrial inner membrane] (Sus scrofa)
815kDa complex [mitochondrial inner membrane] (Sus scrofa)
550kDa complex [mitochondrial inner membrane] (Sus scrofa)
315kDa subcomplex [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Sus scrofa)
315kDa subcomplex [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
550kDa complex [mitochondrial inner membrane] (Sus scrofa)
315kDa subcomplex [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Sus scrofa)
980kDa complex [mitochondrial inner membrane] (Sus scrofa)
815kDa complex [mitochondrial inner membrane] (Sus scrofa)
550kDa complex [mitochondrial inner membrane] (Sus scrofa)
315kDa subcomplex [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 [mitochondrial inner membrane] (Sus scrofa)
IP subcomplex [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Complex I [mitochondrial inner membrane] (Sus scrofa)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Sus scrofa)
Complex I [mitochondrial inner membrane] (Sus scrofa)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Metabolism of proteins (Sus scrofa)
Mitochondrial protein degradation (Sus scrofa)
CLPXP binds mitochondrial matrix proteins (Sus scrofa)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
CLPXP degrades mitochondrial matrix proteins (Sus scrofa)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Sus scrofa)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
NDUFS3 [mitochondrial matrix] (Sus scrofa)
External Reference Information
External Reference
UniProt:A0A286ZNN4
Gene Names
NDUFS3
Reference Genes
ENSEMBL:ENSSSCG00000032081.2
UCSC:A0A286ZNN4 NDUFS3
Other Identifiers
100510948
GO:0003824
GO:0003954
GO:0005215
GO:0005634
GO:0005654
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0012501
GO:0016491
GO:0016604
GO:0016651
GO:0023052
GO:0030308
GO:0031966
GO:0032981
GO:0043226
GO:0065003
GO:0072593
GO:2001243
Ssc.1309.1.S1_at
Ssc.1309.2.S1_a_at
Participates
as a member of
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Sus scrofa)
as an input of
NDUF subunits bind to form the IP subcomplex (Sus scrofa)
as a component of
IP subcomplex [mitochondrial matrix] (Sus scrofa)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Sus scrofa)
Other forms of this molecule
NDUFS3 [cytosol]
Inferred From
NDUFS3 [mitochondrial matrix]
(Homo sapiens)
Cross References
ENSEMBL
ENSSSCG00000032081
,
ENSSSCT00000046945
,
ENSSSCP00000033190
VGNC
90651
PDB
7W4F
,
7W2Y
,
7V2E
,
7VXU
,
7W20
,
7W4L
,
7VY8
,
7V2K
,
7W2U
,
7VB7
,
7V33
,
7V31
,
7W4E
,
7W4G
,
7V32
,
7W4D
,
7VZV
,
7VBZ
,
7V2H
,
7W4C
,
7W1V
,
7VYA
,
7W1Z
,
7W2K
,
7VYN
,
7VYH
,
7W32
,
7W0Y
,
7VWJ
,
7W1P
,
7W4M
,
7W1O
,
7W4N
,
7W0H
,
7W00
,
7VXP
,
7W4Q
,
7V2R
,
7V30
,
7VBN
,
7V2D
,
7V2F
,
7V2C
,
7VZW
,
7W4K
,
7W4J
,
7W1U
,
7W1T
,
7W2L
,
7VZ1
,
7VYF
,
7W0R
,
7W31
,
7W35
,
7W2R
,
7V3M
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text