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HEXB [lysosomal lumen]
Stable Identifier
R-SSC-1605605
Type
Protein [EntityWithAccessionedSequence]
Species
Sus scrofa
Compartment
lysosomal lumen
Synonyms
HEXB(316-556), D0G6X8
Locations in the PathwayBrowser
Expand all
Metabolism (Sus scrofa)
Metabolism of carbohydrates (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Chondroitin sulfate/dermatan sulfate metabolism (Sus scrofa)
CS/DS degradation (Sus scrofa)
HEXA cleaves the terminal GalNAc from DS (Sus scrofa)
bHEXA [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
HEXB cleaves the terminal GalNAc from DS (Sus scrofa)
bHEXB [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
Hyaluronan metabolism (Sus scrofa)
Hyaluronan uptake and degradation (Sus scrofa)
HEXA cleaves the terminal GalNAc from small HA fragments (Sus scrofa)
bHEXA [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
HEXB cleaves the terminal GalNAc from small HA fragments (Sus scrofa)
bHEXB [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
Keratan sulfate/keratin metabolism (Sus scrofa)
Keratan sulfate degradation (Sus scrofa)
HEXA cleaves the terminal GalNAc from keratan sulfate (Sus scrofa)
bHEXA [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
HEXB cleaves the terminal GalNAc from keratan sulfate (Sus scrofa)
bHEXB [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
Metabolism of lipids (Sus scrofa)
Sphingolipid metabolism (Sus scrofa)
Glycosphingolipid metabolism (Sus scrofa)
Glycosphingolipid catabolism (Sus scrofa)
bHEXA hydrolyzes GM2A:GM2 to GM2A:GM3 (Sus scrofa)
bHEXA [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
bHEXA,bHEXB hydrolyze GM2A:GA2 to GM2A:LacCer (Sus scrofa)
bHEXA,bHEXB [lysosomal lumen] (Sus scrofa)
bHEXA [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
bHEXB [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
bHEXA,bHEXB hydrolyze PSAP(195-273):Gb4Cer:PE (Sus scrofa)
bHEXA,bHEXB [lysosomal lumen] (Sus scrofa)
bHEXA [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
bHEXB [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
bHEXA,bHEXS hydrolyze GM2A:SM2 (Sus scrofa)
bHEXA,bHEXS [lysosomal lumen] (Sus scrofa)
bHEXA [lysosomal lumen] (Sus scrofa)
HEXB dimer [lysosomal lumen] (Sus scrofa)
Mature HEXB [lysosomal lumen] (Sus scrofa)
HEXB [lysosomal lumen] (Sus scrofa)
External Reference Information
External Reference
UniProt:D0G6X8
Gene Names
HEXB
Reference Genes
BioGPS Gene:396958 HEXB
ENSEMBL:ENSSSCG00000014073.4
ENSEMBL:ENSSSCG00005009203.1 HEXB
KEGG Gene (Sus scrofa):396958 HEXB
Monarch:396958 HEXB
NCBI Gene:396958 HEXB
Reference Transcript
RefSeq:NM_213921.1 HEXB
Other Identifiers
396958
GO:0001501
GO:0001669
GO:0003824
GO:0004553
GO:0004563
GO:0005576
GO:0005615
GO:0005764
GO:0005773
GO:0005975
GO:0006351
GO:0006355
GO:0006629
GO:0006687
GO:0006689
GO:0006790
GO:0006874
GO:0007040
GO:0007338
GO:0007341
GO:0007605
GO:0007626
GO:0008049
GO:0008152
GO:0008360
GO:0008375
GO:0008654
GO:0009313
GO:0015929
GO:0016020
GO:0016740
GO:0016787
GO:0016798
GO:0019538
GO:0019915
GO:0019953
GO:0022414
GO:0030154
GO:0030203
GO:0030207
GO:0030209
GO:0030214
GO:0031410
GO:0042552
GO:0042582
GO:0042802
GO:0043226
GO:0043615
GO:0045944
GO:0048477
GO:0048856
GO:0048870
GO:0050877
GO:0050885
GO:0050905
GO:0051651
GO:0055065
GO:0060473
GO:0070050
GO:0102148
GO:1901135
GO:1905379
Ssc.3196.1.S1_at
Participates
as a component of
Mature HEXB [lysosomal lumen] (Sus scrofa)
Other forms of this molecule
HEXB [extracellular region]
HEXB [extracellular region]
HEXB [azurophil granule lumen]
HEXB [azurophil granule lumen]
HEXB [lysosomal lumen]
HEXB [lysosomal lumen]
Inferred From
HEXB(316-556) [lysosomal lumen]
(Homo sapiens)
Modified Residues
Name
Inter-chain Crosslink via L-cystine (cross-link) at 360 and 309 (in Homo sapiens)
Coordinate
360
PsiMod Name
L-cystine (cross-link)
PsiMod Definition
A protein modification that effectively cross-links two L-cysteine residues to form L-cystine.
Cross References
RefSeq
NP_999086.1
OpenTargets
ENSG00000049860
Ensembl
ENSSSCT00000015373
,
ENSSSCP00000014965
,
ENSSSCG00000014073
VGNC
88861
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