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Go!
FH [mitochondrial matrix]
Stable Identifier
R-MMU-70980
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
P97807
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Citric acid cycle (TCA cycle) (Mus musculus)
FH tetramer hydrates fumarate to L-malate (Mus musculus)
FH tetramer [mitochondrial matrix] (Mus musculus)
FH [mitochondrial matrix] (Mus musculus)
Metabolism of proteins (Mus musculus)
Mitochondrial protein degradation (Mus musculus)
CLPXP binds mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
FH [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
FH [mitochondrial matrix] (Mus musculus)
CLPXP degrades mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
FH [mitochondrial matrix] (Mus musculus)
LONP1 binds mitochondrial matrix proteins (Mus musculus)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
FH [mitochondrial matrix] (Mus musculus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
FH [mitochondrial matrix] (Mus musculus)
LONP1 degrades mitochondrial matrix proteins (Mus musculus)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
FH [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:P97807
Reference Genes
BioGPS Gene:14194
CTD Gene:14194
ENSEMBL:ENSMUSG00000026526
ENSEMBL:ENSMUSG00000026526.15
KEGG Gene (Mus musculus):14194
Monarch:14194
NCBI Gene:14194
UCSC:P97807
Reference Transcript
RefSeq:NM_010209.2
Other Identifiers
10360443
14194
1424828_a_at
17230153
4510984
4553620
4638262
4730158
4876168
4900473
5052777
5113277
5194178
5281978
5305766
5393155
99148_at
GE33156
GO:0003824
GO:0004333
GO:0005634
GO:0005694
GO:0005737
GO:0005739
GO:0005759
GO:0005829
GO:0006091
GO:0006099
GO:0006106
GO:0006108
GO:0006281
GO:0006974
GO:0016829
GO:0035861
GO:0042393
GO:0043226
GO:0044238
GO:0045239
GO:0048873
GO:0120162
GO:2001034
ILMN_2771754
mMC004822
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
as a component of
FH tetramer [mitochondrial matrix] (Mus musculus)
Inferred From
FH [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_034339.2
IntEnz
4.2.1.2
Ensembl
ENSMUSP00000027810
,
ENSMUST00000027810
,
ENSMUSG00000026526
PRO
P97807
MGI
95530
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