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NDUFS8 [mitochondrial matrix]
Stable Identifier
R-MMU-6788526
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
Q8K3J1
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Mus musculus)
Respiratory electron transport (Mus musculus)
Complex I biogenesis (Mus musculus)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
NDUF subunits bind to form the IP subcomplex (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
NUBPL transfers 4Fe-4S to Complex I subunits (Mus musculus)
NDUF subunits [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
NDUF:4Fe-4S subunits [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS8 [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:Q8K3J1
Reference Genes
BioGPS Gene:225887
ENSEMBL:ENSMUSG00000059734
ENSEMBL:ENSMUSG00000059734.8
KEGG Gene (Mus musculus):225887
Monarch:225887
NCBI Gene:225887
UCSC:Q8K3J1
Reference Transcript
RefSeq:NM_144870.5
RefSeq:NM_001271443.1
RefSeq:NM_001271444.1
Other Identifiers
10464551
1423907_a_at
1423908_at
1434213_x_at
1434579_x_at
1455283_x_at
165405_at
17361032
225887
4353705
4544361
4798027
4916108
5007766
5132552
5163363
5366774
5527399
A_51_P247441
A_55_P2914183
GE130186
GO:0003824
GO:0003954
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0006979
GO:0007005
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0016651
GO:0032981
GO:0042776
GO:0043226
GO:0046872
GO:0051536
GO:0051539
GO:0055086
GO:0065003
GO:0070469
GO:1901135
ILMN_2711734
mMC002820
Participates
as a member of
NDUF subunits [mitochondrial matrix] (Mus musculus)
as a component of
NDUFS8:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
Inferred From
NDUFS8 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_659119.2
,
NP_001258373.1
,
NP_001258372.1
Ensembl
ENSMUSG00000059734
,
ENSMUST00000075092
,
ENSMUST00000236801
,
ENSMUSP00000074600
,
ENSMUSP00000158029
,
ENSMUSP00000158327
,
ENSMUSP00000158541
,
ENSMUST00000235847
,
ENSMUST00000237341
PRO
Q8K3J1
MGI
2385079
PDB
6G2J
,
6G72
,
7AK5
,
7B93
,
7PSA
,
7AK6
,
6ZR2
,
6ZTQ
,
8OLT
,
8OM1
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