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NDUFS2 [mitochondrial matrix]
Stable Identifier
R-MMU-6788520
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
Q91WD5
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Mus musculus)
Respiratory electron transport (Mus musculus)
Complex I biogenesis (Mus musculus)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
NDUF subunits bind to form the IP subcomplex (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
NUBPL transfers 4Fe-4S to Complex I subunits (Mus musculus)
NDUF subunits [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
NDUF:4Fe-4S subunits [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
NDUFAF7:NDUFS2:2x4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
NDUFS2 [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:Q91WD5
Reference Genes
BioGPS Gene:226646
ENSEMBL:ENSMUSG00000013593
ENSEMBL:ENSMUSG00000013593.13
KEGG Gene (Mus musculus):226646
Monarch:226646
NCBI Gene:226646
UCSC:Q91WD5
Reference Transcript
RefSeq:NM_153064.5
Other Identifiers
10360076
1451096_at
17229665
226646
4374964
4378263
4383121
4398147
4402267
4502510
4586749
4606803
4733421
4812761
4869391
4998129
5004702
5045779
5284130
5415934
93972_at
A_51_P393761
A_55_P2106063
GO:0003824
GO:0003954
GO:0005215
GO:0005515
GO:0005634
GO:0005654
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0006979
GO:0007005
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0016651
GO:0019826
GO:0022008
GO:0030154
GO:0031625
GO:0032981
GO:0042063
GO:0042775
GO:0042776
GO:0043226
GO:0046872
GO:0048038
GO:0048856
GO:0051287
GO:0051536
GO:0051539
GO:0055086
GO:0061351
GO:0065003
GO:0070469
GO:0071453
GO:0140299
GO:1901135
ILMN_1224781
ILMN_2704165
aa415929_s_at
mMC019049
Participates
as a member of
NDUF subunits [mitochondrial matrix] (Mus musculus)
as a component of
NDUFS2:4Fe-4S [mitochondrial matrix] (Mus musculus)
Inferred From
NDUFS2 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_694704.1
Ensembl
ENSMUST00000013737
,
ENSMUSP00000013737
,
ENSMUSG00000013593
PRO
Q91WD5
MGI
2385112
PDB
8OM1
,
8OLT
,
7PSA
,
6G72
,
7B93
,
7AK5
,
6G2J
,
6ZR2
,
7AK6
,
6ZTQ
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