Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
ISCU-1 [mitochondrial matrix]
Stable Identifier
R-MMU-1362391
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
Q9D7P6
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Citric acid cycle (TCA cycle) (Mus musculus)
Maturation of TCA enzymes and regulation of TCA cycle (Mus musculus)
Transfer of Fe-S clusters to SDHB (Mus musculus)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
Respiratory electron transport (Mus musculus)
Complex III assembly (Mus musculus)
2Fe-2S is inserted in UQCRFS1 (Mus musculus)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
Mitochondrial iron-sulfur cluster biogenesis (Mus musculus)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Mus musculus)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
Frataxin binds iron (Mus musculus)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Mus musculus)
ISCU-1 [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:Q9D7P6
Reference Genes
BioGPS Gene:66383
ENSEMBL:ENSMUSG00000025825
KEGG:mmu:66383
Monarch:66383
NCBI Gene:66383
UCSC:Q9D7P6
Reference Transcript
RefSeq:NM_025526.4
Other Identifiers
10461108
10524417
1452579_at
17440757
4310272
4763892
4808505
4880393
4910963
5107071
5191634
5204972
5324757
5384888
5488402
5569764
5614421
66383
A_51_P316188
A_55_P2020549
A_55_P2020552
GE121420
GO:0005506
GO:0005737
GO:0005739
GO:0005759
GO:0006879
GO:0008198
GO:0008270
GO:0016226
GO:0042803
GO:0043226
GO:0044571
GO:0044572
GO:0046872
GO:0051536
GO:0051537
GO:0099128
GO:1990229
ILMN_1234425
mMC022796
Participates
as a component of
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Mus musculus)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Mus musculus)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Mus musculus)
Inferred From
ISCU-1 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_079802.1
ENSEMBL
ENSMUST00000026937
,
ENSMUSP00000026937
,
ENSMUSG00000025825
PRO
Q9D7P6
MGI
1913633
PDB
1WFZ
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text