Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
SMIM20 [mitochondrial inner membrane]
Stable Identifier
R-HSA-9865334
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex IV assembly (Homo sapiens)
MT-CO1 and MT-CO2 complexes associate, installing heme moieties (Homo sapiens)
MT-CO1:Cu2+:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
holo-MT-CO1,2 complex [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1 mRNA is translated (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
MT-CO3, COX6A,B,7A and NDUFA4 bind to holo-MT-CO1,2 complex (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
holo-MT-CO1,2 complex [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
Metallochaperone inserts Cu2+ into MT-CO1 (Homo sapiens)
MT-CO1:Cu2+:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
Nascent MT-CO1 binds to MITRAC, Mg2+, PE, CL (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
TIMM21 carries COX4, COX5A, COX6C to MT-CO1:MITRAC (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
MT-CO1:Mg2+:PE:CL:MITRAC:TIMM21:COX4:COX5A:COX6C [mitochondrial inner membrane] (Homo sapiens)
MITRAC [mitochondrial inner membrane] (Homo sapiens)
SMIM20 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q8N5G0 SMIM20
Gene Names
SMIM20, C4orf52, MITRAC7
Chain
chain:1-67, peptide:45-64, peptide:51-64
Reference Genes
BioGPS Gene:389203 SMIM20
COSMIC (genes):SMIM20 SMIM20
CTD Gene:389203 SMIM20
dbSNP Gene:389203 SMIM20
ENSEMBL:ENSG00000250317 SMIM20
HGNC:37260 SMIM20
KEGG:hsa:389203 SMIM20
Monarch:389203 SMIM20
NCBI Gene:389203 SMIM20
OMIM:617465 SMIM20
UCSC:Q8N5G0 SMIM20
Reference Transcript
RefSeq:NM_001145432.3 SMIM20
Other Identifiers
11743267_at
16965628
225014_PM_at
225014_at
2722087
2722088
2722095
2722096
2722098
2722099
2722100
2722101
389203
46996_s_at
51106_at
8094456
A_24_P341222
GE864907
GO:0005515
GO:0005576
GO:0005739
GO:0005743
GO:0016020
GO:0033617
GO:0043226
GO:0065003
HMNXSV003014152
Hs.235026.0.A1_3p_at
ILMN_1652763
TC04000180.hg
Participates
as a component of
MITRAC [mitochondrial inner membrane] (Homo sapiens)
Inferred To
SMIM20 [mitochondrial inner membrane]
(Bos taurus)
SMIM20 [mitochondrial inner membrane]
(Canis familiaris)
SMIM20 [mitochondrial inner membrane]
(Sus scrofa)
Smim20 [mitochondrial inner membrane]
(Mus musculus)
Smim20 [mitochondrial inner membrane]
(Rattus norvegicus)
Ghost homologue of SMIM20 [mitochondrial inner membrane]
(Caenorhabditis elegans)
CG34242-RA [mitochondrial inner membrane]
(Drosophila melanogaster)
Cross References
RefSeq
NP_001138904.1
ENSEMBL
ENSG00000250317
,
ENSP00000427407
,
ENST00000506197
OpenTargets
ENSG00000250317
GeneCards
SMIM20
HPA
ENSG00000250317-SMIM20
PRO
Q8N5G0
Pharos - Targets
Q8N5G0
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text