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SDHAF3 [mitochondrial matrix]
Stable Identifier
R-HSA-9855015
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
Maturation of TCA enzymes and regulation of TCA cycle (Homo sapiens)
SDHA binds to SDHB (Homo sapiens)
FAD-SDHA:SDHB:2Fe-2S:3Fe-4S:4Fe-4S:SDHFA1:SDHFA3 [mitochondrial matrix] (Homo sapiens)
SDHB:2Fe-2S:3Fe-4S:4Fe-4S:SDHAF1:SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHB:2Fe-2S:3Fe-4S:4Fe-4S:SDHAF1:SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHA:SDHB binds to SDHC:SDHD (Homo sapiens)
FAD-SDHA:SDHB:2Fe-2S:3Fe-4S:4Fe-4S:SDHFA1:SDHFA3 [mitochondrial matrix] (Homo sapiens)
SDHB:2Fe-2S:3Fe-4S:4Fe-4S:SDHAF1:SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHAF3 [mitochondrial matrix] (Homo sapiens)
Transfer of Fe-S clusters to SDHB (Homo sapiens)
SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHB:2Fe-2S:3Fe-4S:4Fe-4S:SDHAF1:SDHAF3 [mitochondrial matrix] (Homo sapiens)
SDHAF3 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9NRP4 SDHAF3
Gene Names
SDHAF3, ACN9, DC11
Chain
transit peptide:1-30, chain:31-125
Reference Genes
BioGPS Gene:57001 SDHAF3
COSMIC (genes):SDHAF3 SDHAF3
CTD Gene:57001 SDHAF3
dbSNP Gene:57001 SDHAF3
ENSEMBL:ENSG00000196636 SDHAF3
HGNC:21752 SDHAF3
KEGG:hsa:57001 SDHAF3
Monarch:57001 SDHAF3
NCBI Gene:57001 SDHAF3
OMIM:615773 SDHAF3
UCSC:Q9NRP4 SDHAF3
Reference Transcript
RefSeq:NM_020186.2 SDHAF3
Other Identifiers
11722226_s_at
17048686
218981_PM_at
218981_at
3013960
3013961
3013962
3013972
3013973
3013976
3013977
3013978
3013979
57001
62124_at
A_23_P59528
GE62947
GO:0005739
GO:0005758
GO:0005759
GO:0006105
GO:0006111
GO:0034553
GO:0043226
GO:0065003
HMNXSV003021390
ILMN_1771348
ILMN_2134039
PH_hs_0003131
TC07000578.hg
g9910179_3p_at
g9910179_3p_x_at
Participates
as an output of
SDHA:SDHB binds to SDHC:SDHD (Homo sapiens)
as a component of
SDHB:2Fe-2S:3Fe-4S:4Fe-4S:SDHAF1:SDHAF3 [mitochondrial matrix] (Homo sapiens)
as an input of
Transfer of Fe-S clusters to SDHB (Homo sapiens)
Inferred To
SDHAF3 [mitochondrial matrix]
(Bos taurus)
SDHAF3 [mitochondrial matrix]
(Sus scrofa)
R4GHE6 [mitochondrial matrix]
(Gallus gallus)
P91989 [mitochondrial matrix]
(Caenorhabditis elegans)
SDH7 [mitochondrial matrix]
(Saccharomyces cerevisiae)
acn9 [mitochondrial matrix]
(Dictyostelium discoideum)
Sdhaf3 [mitochondrial matrix]
(Drosophila melanogaster)
Sdhaf3 [mitochondrial matrix]
(Mus musculus)
Sdhaf3 [mitochondrial matrix]
(Rattus norvegicus)
Ghost homologue of SDHAF3 [mitochondrial matrix]
(Canis familiaris)
sdhaf3 [mitochondrial matrix]
(Danio rerio)
sdhaf3 [mitochondrial matrix]
(Xenopus tropicalis)
Q9P7Y2 [mitochondrial matrix]
(Schizosaccharomyces pombe)
Cross References
RefSeq
NP_064571.1
ENSEMBL
ENST00000432641
,
ENSP00000414066
OpenTargets
ENSG00000196636
HPA
ENSG00000196636-SDHAF3
PRO
Q9NRP4
Pharos - Targets
Q9NRP4
Interactors (4)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P21912 SDHB
2
SDHB [mitochondrial inner membrane]
(R-HSA-70985)
SDHB [mitochondrial matrix]
(R-HSA-9854983)
0.643
4
UniProt:O14561 NDUFAB1
4
octanoyl-S112-NDUFAB1 [mitochondrial inner membrane]
(R-HSA-9857608)
NDUFAB1 [mitochondrial inner membrane]
(R-HSA-163925)
PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
(R-HSA-8933545)
Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
(R-HSA-8934586)
0.643
6
UniProt:Q5VUM1 SDHAF4
1
SDHAF4 [mitochondrial matrix]
(R-HSA-9854972)
0.527
2
UniProt:P31040 SDHA
2
FAD-SDHA [mitochondrial matrix]
(R-HSA-70983)
SDHA [mitochondrial matrix]
(R-HSA-9854690)
0.527
2
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