Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
NDUFA13(41-49) [mitochondrial inner membrane]
Stable Identifier
R-HSA-9839958
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 13, NDUAD_HUMAN
Locations in the PathwayBrowser for interactor UniProt:P23786 CPT2
Expand all
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
HTRA2 degrades NDUFA13 (GRIM-19) (Homo sapiens)
NDUFA13(41-49) [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9P0J0 NDUFA13
Gene Names
NDUFA13, GRIM19, CDA016, CGI-39
Chain
initiator methionine:, chain:2-144
Reference Genes
BioGPS Gene:51079 NDUFA13
COSMIC (genes):NDUFA13 NDUFA13
CTD Gene:51079 NDUFA13
dbSNP Gene:51079 NDUFA13
ENSEMBL:ENSG00000186010 NDUFA13
HGNC:17194 NDUFA13
KEGG:hsa:51079 NDUFA13
Monarch:51079 NDUFA13
NCBI Gene:51079 NDUFA13
OMIM:609435 NDUFA13
UCSC:Q9P0J0 NDUFA13
Reference Transcript
RefSeq:NM_015965.6 NDUFA13
Other Identifiers
11720341_at
11720342_s_at
11757719_x_at
11762332_at
11762333_x_at
16860047
220864_PM_s_at
220864_s_at
3825824
3825825
3825826
3825829
3825830
3825831
3825832
3825833
3825834
3825835
3825836
3825837
3825839
3825840
3825857
3825859
45339_at
51079
8027205
A_23_P119627
A_33_P3359061
GE82057
GO:0005515
GO:0005524
GO:0005634
GO:0005654
GO:0005737
GO:0005739
GO:0005743
GO:0006091
GO:0006355
GO:0006886
GO:0006915
GO:0007005
GO:0009060
GO:0012501
GO:0016020
GO:0031966
GO:0032981
GO:0035458
GO:0042776
GO:0043226
GO:0045039
GO:0045271
GO:0045732
GO:0045892
GO:0055086
GO:0061024
GO:0061133
GO:0065003
GO:0071300
GO:0097191
GO:0098772
GO:0098803
GO:1900119
GO:1901135
HMNXSV003044952
ILMN_1767139
PH_hs_0032456
g7705733_3p_a_at
Participates
as an output of
HTRA2 degrades NDUFA13 (GRIM-19) (Homo sapiens)
Other forms of this molecule
NDUFA13 [mitochondrial inner membrane]
NDUFA13(100-108) [mitochondrial inner membrane]
NDUFA13(109-144) [mitochondrial inner membrane]
NDUFA13(2-19) [mitochondrial inner membrane]
NDUFA13(69-99) [mitochondrial inner membrane]
NDUFA13(20-40) [mitochondrial inner membrane]
NDUFA13(50-68) [mitochondrial inner membrane]
Inferred To
Homologues of NDUFA13(41-49) [mitochondrial inner membrane]
(Rattus norvegicus)
NDUFA13 [mitochondrial inner membrane]
(Bos taurus)
NDUFA13 [mitochondrial inner membrane]
(Canis familiaris)
NDUFA13(41-49) [mitochondrial inner membrane]
(Sus scrofa)
Ndufa13 [mitochondrial inner membrane]
(Mus musculus)
Ndufa13 [mitochondrial inner membrane]
(Rattus norvegicus)
ND-B16.6 [mitochondrial inner membrane]
(Drosophila melanogaster)
Cross References
ENSEMBL
ENSP00000423673
,
ENST00000507754
OpenTargets
ENSG00000186010
HPA
ENSG00000186010-NDUFA13
PRO
Q9P0J0
Pharos - Targets
Q9P0J0
Orphanet
NDUFA13
PDB
5XTI
,
5XTH
,
5XTB
,
5XTC
,
5XTD
HMDB Protein
HMDBP00190
Interactors (31)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q9P032 NDUFAF4
1
NDUFAF4 [mitochondrial inner membrane]
(R-HSA-5689124)
0.725
6
UniProt:O43464 HTRA2
1
HTRA2 [mitochondrial intermembrane space]
(R-HSA-56655)
0.674
7
UniProt:P42858 HTT
1
HTT [nucleoplasm]
(R-HSA-9023590)
0.666
4
UniProt:Q9Y375 NDUFAF1
1
NDUFAF1 [mitochondrial inner membrane]
(R-HSA-5689050)
0.643
4
UniProt:Q9UI09 NDUFA12
1
NDUFA12 [mitochondrial inner membrane]
(R-HSA-59864)
0.643
5
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.643
7
UniProt:O95298 NDUFC2
3
NDUFC2 [mitochondrial inner membrane]
(R-HSA-59860)
NDUFC2 [plasma membrane]
(R-HSA-6806276)
NDUFC2 [azurophil granule membrane]
(R-HSA-6799211)
0.643
4
UniProt:Q9H845 ACAD9
1
ACAD9 [mitochondrial inner membrane]
(R-HSA-5689049)
0.643
4
UniProt:Q9BQ95 ECSIT
2
ECSIT [cytosol]
(R-HSA-168064)
ECSIT [mitochondrial inner membrane]
(R-HSA-5689047)
0.643
4
UniProt:O43181 NDUFS4
1
NDUFS4 [mitochondrial inner membrane]
(R-HSA-163946)
0.643
4
UniProt:O75251 NDUFS7
1
NDUFS7 [mitochondrial matrix]
(R-HSA-6788521)
0.643
4
UniProt:O43678 NDUFA2
1
NDUFA2 [mitochondrial inner membrane]
(R-HSA-60178)
0.564
3
UniProt:Q9HC29 NOD2
1
NOD2 [cytosol]
(R-HSA-168411)
0.543
6
UniProt:P49821 NDUFV1
1
NDUFV1 [mitochondrial inner membrane]
(R-HSA-163926)
0.527
2
UniProt:Q16795 NDUFA9
1
NDUFA9 [mitochondrial matrix]
(R-HSA-163942)
0.527
2
UniProt:O43920 NDUFS5
1
NDUFS5 [mitochondrial inner membrane]
(R-HSA-60226)
0.527
2
UniProt:Q16718 NDUFA5
2
NDUFA5 [endoplasmic reticulum membrane]
(R-HSA-9714749)
NDUFA5 [mitochondrial inner membrane]
(R-HSA-60599)
0.527
2
UniProt:P23786 CPT2
1
CPT2 [mitochondrial inner membrane]
(R-HSA-200994)
0.527
2
UniProt:P01037 CYTN
0.527
2
UniProt:O75306 NDUFS2
1
NDUFS2 [mitochondrial matrix]
(R-HSA-6788520)
0.527
2
UniProt:O75380 NDUFS6
1
NDUFS6 [mitochondrial inner membrane]
(R-HSA-163922)
0.527
3
UniProt:Q9NPL8 TIMMDC1
1
TIMMDC1 [mitochondrial inner membrane]
(R-HSA-5689720)
0.527
3
UniProt:P03905 MT-ND4
1
MT-ND4 [mitochondrial inner membrane]
(R-HSA-60561)
0.527
3
UniProt:P56556 NDUFA6
1
NDUFA6 [mitochondrial inner membrane]
(R-HSA-59932)
0.527
2
UniProt:O43674 NDUFB5
1
NDUFB5 [mitochondrial inner membrane]
(R-HSA-163944)
0.527
3
UniProt:O43676 NDUFB3
1
NDUFB3 [mitochondrial inner membrane]
(R-HSA-59930)
0.527
2
UniProt:O00217 NDUFS8
1
NDUFS8 [mitochondrial matrix]
(R-HSA-6788526)
0.527
3
UniProt:Q9BU61 NDUFAF3
1
NDUFAF3 [mitochondrial inner membrane]
(R-HSA-5689126)
0.527
3
UniProt:O95167 NDUFA3
1
NDUFA3 [mitochondrial inner membrane]
(R-HSA-60180)
0.527
3
UniProt:Q8IUX1 TMEM126B
1
TMEM126B [mitochondrial inner membrane]
(R-HSA-5689046)
0.527
3
UniProt:O95182 NDUFA7
1
NDUFA7 [mitochondrial inner membrane]
(R-HSA-59858)
0.527
3
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text