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Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
Stable Identifier
R-HSA-8934586
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase 9.6 kDa subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
MCAT transfers Mal from Mal-CoA to NDUFAB1 (Homo sapiens)
Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O14561 NDUFAB1
Gene Names
NDUFAB1
Chain
transit peptide:1-68, chain:69-156
Reference Genes
BioGPS Gene:4706 NDUFAB1
COSMIC (genes):NDUFAB1 NDUFAB1
CTD Gene:4706 NDUFAB1
dbSNP Gene:4706 NDUFAB1
ENSEMBL:ENSG00000004779 NDUFAB1
ENSEMBL_homo_sapiens_GENE:ENSG00000004779 NDUFAB1
HGNC:7694 NDUFAB1
KEGG Gene (Homo sapiens):4706 NDUFAB1
Monarch:4706 NDUFAB1
NCBI Gene:4706 NDUFAB1
OMIM:603836 NDUFAB1
UCSC:O14561 NDUFAB1
Reference Transcript
RefSeq:NM_005003.2 NDUFAB1
Other Identifiers
0005900647
11715616_a_at
16825097
202077_at
2DNW
35297_at
3685308
3685309
3685310
3685312
3685313
3685322
4706
54364
5OOL
5OOM
5XTB
5XTC
5XTD
5XTH
5XTI
8000323
A_23_P140960
AAC05814
AAD23566
AAH58920
AC002400
AF087660
AK311877
BAG34818
BC058920
CCDS10614
CH471145
EAW55816
ENSG00000004779
ENSP00000007516
ENSP00000458770
ENST00000007516
ENST00000570319
EntrezGene:4706
g4826851_3p_at
GE62078
GO:0000035
GO:0000036
GO:0003674
GO:0005504
GO:0005509
GO:0005515
GO:0005575
GO:0005622
GO:0005623
GO:0005634
GO:0005654
GO:0005737
GO:0005739
GO:0005743
GO:0005747
GO:0005759
GO:0005762
GO:0005829
GO:0005840
GO:0005975
GO:0006091
GO:0006120
GO:0006464
GO:0006629
GO:0006631
GO:0006633
GO:0007005
GO:0008137
GO:0008150
GO:0008289
GO:0009058
GO:0009245
GO:0009249
GO:0016491
GO:0022607
GO:0031177
GO:0031966
GO:0032981
GO:0032991
GO:0034641
GO:0043167
GO:0043226
GO:0044281
GO:0051604
GO:0055114
GO:0065003
GO:0070469
H3BNE8
HGNC:7694
HPA054364
I3L505
ILMN_1755521
ILMN_2179018
IPR003231
IPR006162
IPR009081
IPR036736
MIM:603836
NDUFAB1
NDUFAB1-201
NDUFAB1-205
NM_005003
NP_004994
PF00550
PH_hs_0000572
PH_hs_0035327
TC16000966.hg
uc002dlw.4
uc059sda.1
UPI0000125321
XM_011545856
XP_011544158
Participant Of
output
MCAT transfers Mal from Mal-CoA to NDUFAB1
Other forms of this molecule
NDUFAB1 [mitochondrial inner membrane]
PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
Inferred To
Homologues of Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Arabidopsis thaliana)
Homologues of Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Canis familiaris)
Homologues of Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Danio rerio)
Homologues of Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Oryza sativa)
Homologues of Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Sus scrofa)
Homologues of Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Xenopus tropicalis)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Arabidopsis thaliana)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Bos taurus)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Caenorhabditis elegans)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Canis familiaris)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Danio rerio)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Dictyostelium discoideum)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Drosophila melanogaster)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Gallus gallus)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Mus musculus)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Oryza sativa)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Plasmodium falciparum)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Rattus norvegicus)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Saccharomyces cerevisiae)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Schizosaccharomyces pombe)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Sus scrofa)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Taeniopygia guttata)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Xenopus tropicalis)
Modified Residues
Name
O-phosphopantetheine-L-serine (S-malonyl-4'-phosphopantetheine) at 112
Coordinate
112
Modification
S-malonyl-4'-phosphopantetheine
PsiMod Name
O-phosphopantetheine-L-serine [MOD:00159]
PsiMod Definition
A protein modification that effectively converts an L-serine residue to O-phosphopantetheine-L-serine.
Cross References
RefSeq
NP_004994.1
OpenTargets
ENSG00000004779
GeneCards
O14561
PRO
O14561
Orphanet
24742
HMDB Protein
HMDBP00174
PDB
5XTB
,
5XTD
,
5XTI
,
5OOM
,
2DNW
,
5OOL
,
5XTH
,
5XTC
Interactors (30)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q9GZT3 SLIRP
0.488
2
UniProt:Q6PF18 MORN3
0.488
2
UniProt:P25791-3 LMO2
0.488
2
UniProt:Q96NM4-3 TOX2
0.488
2
UniProt:Q8N4L8 CCD24
0.488
2
UniProt:P26441 CNTF
1
CNTF [extracellular region]
(R-HSA-5696441)
0.488
2
UniProt:Q86VK4-3 ZNF410
0.488
2
UniProt:O43711 TLX3
0.488
2
UniProt:P17023 ZNF19
1
ZNF19 [nucleoplasm]
(R-HSA-974992)
0.488
2
IntAct:EBI-12104350 MBLAC1
0.488
2
UniProt:P17980 PSMC3
5
PSMC3 [extracellular region]
(R-HSA-6806496)
PSMC3 [secretory granule lumen]
(R-HSA-6800917)
PSMC3 [ficolin-1-rich granule lumen]
(R-HSA-6800429)
PSMC3 [cytosol]
(R-HSA-68774)
PSMC3 [nucleoplasm]
(R-HSA-174313)
0.488
4
UniProt:Q08AM6 VAC14
3
VAC14 [early endosome membrane]
(R-HSA-1806207)
VAC14 [late endosome membrane]
(R-HSA-1806219)
VAC14 [Golgi membrane]
(R-HSA-1806235)
0.488
2
UniProt:Q3KNS6-3 Q3KNS63
0.488
2
UniProt:Q8TBB1 LNX1
1
LNX1 [cytosol]
(R-HSA-8851641)
0.488
2
UniProt:Q9NVV9 THAP1
0.488
2
UniProt:Q13643 FHL3
0.488
2
UniProt:Q16656-4 NRF1
0.488
2
UniProt:Q9BQA5 HINFP
0.488
2
UniProt:Q96PG8 BBC3B
0.488
2
UniProt:Q5H9J7 BEX5
0.488
2
UniProt:Q96HA8 NTAQ1
0.488
2
UniProt:O43482 OIP5
1
OIP5 [nucleoplasm]
(R-HSA-606286)
0.488
2
UniProt:Q08043 ACTN3
1
ACTN3 [cytosol]
(R-HSA-390565)
0.488
2
UniProt:Q9BSK4 FEM1A
1
FEM1A [cytosol]
(R-HSA-8863141)
0.488
2
IntAct:EBI-17517666 EIF3B
0.488
2
UniProt:Q96I34 PP16A
0.488
2
UniProt:Q7L273 KCTD9
0.488
2
UniProt:Q969H6 POP5
1
POP5 [nucleoplasm]
(R-HSA-5696783)
0.488
2
UniProt:Q53EP0-3 FNDC3B
0.488
2
UniProt:Q86X59 CQ082
0.488
2
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