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Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
Stable Identifier
R-HSA-8934586
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase 9.6 kDa subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
MCAT transfers Mal from Mal-CoA to NDUFAB1 (Homo sapiens)
Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O14561 NDUFAB1
Gene Names
NDUFAB1
Chain
transit peptide:1-68, chain:69-156
Reference Genes
BioGPS Gene:4706 NDUFAB1
COSMIC (genes):NDUFAB1 NDUFAB1
CTD Gene:4706 NDUFAB1
dbSNP Gene:4706 NDUFAB1
ENSEMBL:ENSG00000004779.10 NDUFAB1
HGNC:7694 NDUFAB1
KEGG Gene (Homo sapiens):4706 NDUFAB1
Monarch:4706 NDUFAB1
NCBI Gene:4706 NDUFAB1
OMIM:603836 NDUFAB1
UCSC:O14561 NDUFAB1
Reference Transcript
RefSeq:NM_005003.2 NDUFAB1
Other Identifiers
0005900647
11715616_a_at
16825097
202077_PM_at
202077_at
35297_at
3685308
3685309
3685310
3685312
3685313
3685322
4706
8000323
GE62078
GO:0000035
GO:0000036
GO:0005504
GO:0005509
GO:0005515
GO:0005622
GO:0005634
GO:0005654
GO:0005737
GO:0005739
GO:0005743
GO:0005747
GO:0005759
GO:0005762
GO:0005829
GO:0005840
GO:0006091
GO:0006120
GO:0006629
GO:0006631
GO:0006633
GO:0006790
GO:0007005
GO:0008289
GO:0009060
GO:0009249
GO:0016226
GO:0031966
GO:0032981
GO:0032991
GO:0036211
GO:0042776
GO:0043226
GO:0044281
GO:0051604
GO:0055086
GO:0065003
GO:0070469
GO:0071704
GO:0140104
GO:1901135
GO:1990229
HMNXSV003011323
ILMN_1755521
ILMN_2179018
PH_hs_0000572
TC16000966.hg
g4826851_3p_at
Participates
as an output of
MCAT transfers Mal from Mal-CoA to NDUFAB1 (Homo sapiens)
Other forms of this molecule
PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
NDUFAB1 [mitochondrial inner membrane]
Inferred To
phospho-ndufab1 [mitochondrial inner membrane]
(Dictyostelium discoideum)
phospho-ndufab1 [mitochondrial inner membrane]
(Xenopus tropicalis)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
(Caenorhabditis elegans)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
(Canis familiaris)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
(Danio rerio)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
(Plasmodium falciparum)
phospho-Mal-PPANT-S112-NDUFAB1 [mitochondrial inner membrane]
(Schizosaccharomyces pombe)
phospho-NDUFAB1 [mitochondrial inner membrane]
(Bos taurus)
phospho-NDUFAB1 [mitochondrial inner membrane]
(Gallus gallus)
phospho-NDUFAB1 [mitochondrial inner membrane]
(Sus scrofa)
phospho-ACP1 [mitochondrial inner membrane]
(Saccharomyces cerevisiae)
phospho-ND-ACP [mitochondrial inner membrane]
(Drosophila melanogaster)
phospho-Ndufab1 [mitochondrial inner membrane]
(Mus musculus)
phospho-Ndufab1 [mitochondrial inner membrane]
(Rattus norvegicus)
Modified Residues
Name
O-phosphopantetheine-L-serine (S-malonyl-4'-phosphopantetheine) at 112
Coordinate
112
Modification
S-malonyl-4'-phosphopantetheine
PsiMod Name
O-phosphopantetheine-L-serine [MOD:00159]
PsiMod Definition
A protein modification that effectively converts an L-serine residue to O-phosphopantetheine-L-serine.
Cross References
RefSeq
NP_004994.1
OpenTargets
ENSG00000004779
GeneCards
O14561
HPA
ENSG00000004779-NDUFAB1
Ensembl
ENSP00000458770
,
ENST00000570319
,
ENSP00000007516
,
ENST00000007516
,
ENSG00000004779
PRO
O14561
Pharos - Targets
O14561
Orphanet
24742
HMDB Protein
HMDBP00174
PDB
7PD3
,
7O9M
,
7ODT
,
7ODS
,
7OF2
,
5XTB
,
7OI9
,
7O9K
,
7OI8
,
7ODR
,
7OF0
,
7A5J
,
5XTH
,
5OOL
,
2DNW
,
7OIE
,
7OF7
,
7OI7
,
5OOM
,
7OID
,
5XTI
,
5XTC
,
7QH6
,
6ODD
,
7OF5
,
7OF3
,
7OI6
,
7A5H
,
7OIC
,
5XTD
Interactors (39)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q9GZT3 SLIRP
0.675
4
UniProt:Q6PF18 MORN3
0.556
3
UniProt:P25791-3 LMO2
0.556
3
UniProt:Q96NM4-3 TOX2
0.556
3
UniProt:Q8N4L8 CCD24
0.556
3
UniProt:O43711 TLX3
0.556
5
UniProt:Q86VK4-3 ZNF410
0.556
3
UniProt:P17980 PSMC3
5
PSMC3 [secretory granule lumen]
(R-HSA-6800917)
PSMC3 [extracellular region]
(R-HSA-6806496)
PSMC3 [ficolin-1-rich granule lumen]
(R-HSA-6800429)
PSMC3 [nucleoplasm]
(R-HSA-174313)
PSMC3 [cytosol]
(R-HSA-68774)
0.556
6
UniProt:P17023 ZNF19
1
ZNF19 [nucleoplasm]
(R-HSA-974992)
0.556
3
UniProt:Q08AM6 VAC14
3
VAC14 [Golgi membrane]
(R-HSA-1806235)
VAC14 [early endosome membrane]
(R-HSA-1806207)
VAC14 [late endosome membrane]
(R-HSA-1806219)
0.556
3
IntAct:EBI-22421838 CCSB ORF ID
0.556
3
IntAct:EBI-22608899 CCSB ORF ID
0.556
3
UniProt:Q3KNS6-3 Q3KNS63
0.556
3
UniProt:Q8TBB1 LNX1
1
LNX1 [cytosol]
(R-HSA-8851641)
0.556
3
UniProt:Q86UR1-2 NOXA1
0.556
3
UniProt:Q9NVV9 THAP1
0.556
3
UniProt:Q969H6 POP5
1
POP5 [nucleoplasm]
(R-HSA-5696783)
0.556
3
UniProt:Q53EP0-3 FNDC3B
0.556
5
UniProt:Q7L273 KCTD9
0.556
3
UniProt:Q96I34 PP16A
0.556
3
UniProt:Q08043 ACTN3
1
ACTN3 [cytosol]
(R-HSA-390565)
0.556
3
UniProt:Q9BSK4 FEM1A
1
FEM1A [cytosol]
(R-HSA-8863141)
0.556
3
UniProt:O43482 OIP5
1
OIP5 [nucleoplasm]
(R-HSA-606286)
0.556
3
UniProt:Q96HA8 NTAQ1
0.556
3
UniProt:Q5H9J7 BEX5
0.556
3
UniProt:Q96PG8 BBC3B
0.556
3
UniProt:Q9BQA5 HINFP
0.556
3
UniProt:Q16656-4 NRF1
0.556
3
UniProt:Q13643 FHL3
0.556
5
UniProt:P26441 CNTF
1
CNTF [extracellular region]
(R-HSA-5696441)
0.556
3
UniProt:Q9H2W6 MRPL46
1
MRPL46 [mitochondrial inner membrane]
(R-HSA-5368247)
0.528
2
UniProt:Q16540 MRPL23
1
MRPL23 [mitochondrial inner membrane]
(R-HSA-5368179)
0.528
2
UniProt:Q9NU23 LYRM2
0.527
5
UniProt:Q6IPR1 ETFR1
0.527
5
UniProt:Q9NRP4 SDHF3
0.527
5
UniProt:Q9HD34 LYRM4
1
LYRM4 [mitochondrial matrix]
(R-HSA-1362392)
0.527
5
UniProt:Q5U5X0 LYRM7
0.527
5
UniProt:Q96EH3 MASU1
0.488
2
UniProt:L0R8F8 MIDUO
0.488
2
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