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COQ4 [mitochondrial inner membrane]
Stable Identifier
R-HSA-8932995
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
fullName evidence="1"Ubiquinone biosynthesis protein COQ4 homolog, mitochondrial, COQ4_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ3 methylates DHDB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ4 [mitochondrial inner membrane] (Homo sapiens)
COQ3 methylates DeMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ4 [mitochondrial inner membrane] (Homo sapiens)
COQ4 decarboxylates MHDB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ4 [mitochondrial inner membrane] (Homo sapiens)
COQ4 [mitochondrial inner membrane] (Homo sapiens)
COQ5 methylates MDMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ4 [mitochondrial inner membrane] (Homo sapiens)
COQ6 hydroxylates DHB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ4 [mitochondrial inner membrane] (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ4 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9Y3A0 COQ4
Gene Names
COQ4, CGI-92
Chain
transit peptide:1-30, chain:31-265
Reference Genes
BioGPS Gene:51117 COQ4
COSMIC (genes):COQ4 COQ4
CTD Gene:51117 COQ4
dbSNP Gene:51117 COQ4
ENSEMBL:ENSG00000167113 COQ4
HGNC:19693 COQ4
KEGG:hsa:51117 COQ4
Monarch:51117 COQ4
NCBI Gene:51117 COQ4
OMIM:612898 COQ4
UCSC:Q9Y3A0 COQ4
Reference Transcript
RefSeq:NM_016035.4 COQ4
Other Identifiers
11744283_a_at
11761225_a_at
17089593
218328_PM_at
218328_at
228931_PM_at
228931_at
3190340
3190341
3190342
3190343
3190344
3190345
3190347
3190348
3190349
3190350
3190351
3190352
3190357
3190358
3190359
3190360
3190362
3190363
3190365
49359_at
51117
62205_s_at
62206_i_at
8158214
A_33_P3392330
GE61089
GO:0003824
GO:0005515
GO:0005739
GO:0005743
GO:0006744
GO:0016829
GO:0031314
GO:0032991
GO:0036169
GO:0043226
GO:0110142
HMNXSV003031899
HMNXSV003044123
Hs.20159.1.S1_3p_at
PH_hs_0039284
TC09000685.hg
TC09002278.hg
g7705806_3p_at
Participates
as a component of
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
Inferred To
COQ4 [mitochondrial inner membrane]
(Bos taurus)
COQ4 [mitochondrial inner membrane]
(Canis familiaris)
COQ4 [mitochondrial inner membrane]
(Gallus gallus)
COQ4 [mitochondrial inner membrane]
(Saccharomyces cerevisiae)
COQ4 [mitochondrial inner membrane]
(Sus scrofa)
Coq4 [mitochondrial inner membrane]
(Drosophila melanogaster)
Coq4 [mitochondrial inner membrane]
(Mus musculus)
Coq4 [mitochondrial inner membrane]
(Rattus norvegicus)
coq4 [mitochondrial inner membrane]
(Danio rerio)
coq4 [mitochondrial inner membrane]
(Dictyostelium discoideum)
coq4 [mitochondrial inner membrane]
(Schizosaccharomyces pombe)
coq4 [mitochondrial inner membrane]
(Xenopus tropicalis)
coq-4 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Cross References
RefSeq
NP_057119.2
ENSEMBL
ENSP00000300452
,
ENST00000300452
OpenTargets
ENSG00000167113
HPA
ENSG00000167113-COQ4
PRO
Q9Y3A0
Pharos - Targets
Q9Y3A0
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