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PXLP-PYGM [cytosol]
Stable Identifier
R-HSA-71537
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
cytosol
Synonyms
PYGM, glycogen phosphorylase, muscle form , Myophosphorylase
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycogen metabolism (Homo sapiens)
Glycogen breakdown (glycogenolysis) (Homo sapiens)
PYGM b dimer:AMP complex <=> PYGM dimer, b form + 2 AMP (Homo sapiens)
PYGM b dimer:AMP [cytosol] (Homo sapiens)
PXLP-PYGM [cytosol] (Homo sapiens)
PYGM dimer, b form [cytosol] (Homo sapiens)
PXLP-PYGM [cytosol] (Homo sapiens)
PYGM dimer, b form + 2 AMP <=> PYGM b dimer:AMP complex (Homo sapiens)
PYGM b dimer:AMP [cytosol] (Homo sapiens)
PXLP-PYGM [cytosol] (Homo sapiens)
PYGM dimer, b form [cytosol] (Homo sapiens)
PXLP-PYGM [cytosol] (Homo sapiens)
glycogen phosphorylase (PYGM) dimer b + 2 ATP => glycogen phosphorylase (PYGM) dimer a + 2 ADP (Homo sapiens)
PYGM dimer, b form [cytosol] (Homo sapiens)
PXLP-PYGM [cytosol] (Homo sapiens)
glycogen-glycogenin-1 + n orthophosphate => limit dextrin-glycogenin-1 + n D-glucose 1-phosphate [PYGM,PYGB] (Homo sapiens)
active PYGM and PYGB dimers [cytosol] (Homo sapiens)
PYGM b dimer:AMP [cytosol] (Homo sapiens)
PXLP-PYGM [cytosol] (Homo sapiens)
poly((1,4)-alpha-glycosyl) glycogenin-1 + n orthophosphate => glycogenin-1 + n D-glucose 1-phosphate [PYGM,PYGB] (Homo sapiens)
active PYGM and PYGB dimers [cytosol] (Homo sapiens)
PYGM b dimer:AMP [cytosol] (Homo sapiens)
PXLP-PYGM [cytosol] (Homo sapiens)
External Reference Information
External Reference
UniProt:P11217 PYGM
Gene Names
PYGM
Chain
initiator methionine:1, chain:2-842
Reference Genes
BioGPS Gene:5837 PYGM
COSMIC (genes):PYGM PYGM
CTD Gene:5837 PYGM
dbSNP Gene:5837 PYGM
ENSEMBL:ENSG00000068976 PYGM
ENSEMBL:ENSG00000068976.14 PYGM
HGNC:9726 PYGM
KEGG Gene (Homo sapiens):5837 PYGM
Monarch:5837 PYGM
NCBI Gene:5837 PYGM
OMIM:608455 PYGM
UCSC:P11217 PYGM
Reference Transcript
RefSeq:NM_005609.3 PYGM
RefSeq:NM_001164716.1 PYGM
Other Identifiers
11724200_a_at
16739979
205577_PM_at
205577_at
3377017
3377018
3377019
3377020
3377023
3377025
3377026
3377027
3377028
3377029
3377030
3377031
3377032
3377034
3377035
3377036
3377038
3377039
3377040
3377041
3377042
40057_at
5837
7949124
A_23_P52657
GE60545
GO:0000166
GO:0003824
GO:0004645
GO:0005515
GO:0005576
GO:0005615
GO:0005737
GO:0005829
GO:0005975
GO:0005977
GO:0005980
GO:0006091
GO:0008152
GO:0008184
GO:0016740
GO:0016757
GO:0030170
GO:0043226
GO:0070062
GO:0102250
GO:0102499
ILMN_1720849
PH_hs_0009271
TC11001910.hg
g5032008_3p_at
Participates
as a component of
PYGM dimer, b form [cytosol] (Homo sapiens)
PYGM b dimer:AMP [cytosol] (Homo sapiens)
Other forms of this molecule
PXLP-p-S15-PYGM [cytosol]
Inferred To
Homologues of PXLP-PYGM [cytosol]
(Dictyostelium discoideum)
glpD [cytosol]
(Dictyostelium discoideum)
pygb [cytosol]
(Xenopus tropicalis)
zgc:63642 [cytosol]
(Danio rerio)
GPH1 [cytosol]
(Saccharomyces cerevisiae)
PXLP-PYGM [cytosol]
(Canis familiaris)
PXLP-PYGM [cytosol]
(Dictyostelium discoideum)
PXLP-PYGM [cytosol]
(Drosophila melanogaster)
PXLP-PYGM [cytosol]
(Mus musculus)
PXLP-PYGM [cytosol]
(Rattus norvegicus)
PXLP-PYGM [cytosol]
(Sus scrofa)
pygl-1 [cytosol]
(Caenorhabditis elegans)
PYGM [cytosol]
(Bos taurus)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at 681
Coordinate
681
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
RefSeq
NP_001158188.1
,
NP_005600.1
OpenTargets
ENSG00000068976
ZINC - Substances
PYGM_HUMAN
ZINC target
P11217
PRO
P11217
PDB
1Z8D
ZINC - Investigational
PYGM_HUMAN
GeneCards
P11217
HPA
ENSG00000068976-PYGM
Ensembl
ENSG00000068976
,
ENSP00000366650
,
ENST00000377432
,
ENST00000164139
,
ENSP00000164139
Pharos - Targets
P11217
ZINC - Predictions - Purchasable
PYGM_HUMAN
Orphanet
15177
HMDB Protein
HMDBP00373
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