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GATM [mitochondrial intermembrane space]
Stable Identifier
R-HSA-71267
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial intermembrane space
Synonyms
glycine amidinotransferase, arginine:glycine amidinotransferase, L- arginine:glycine amidinotransferase, Transamidinase, AT
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Creatine metabolism (Homo sapiens)
arginine + glycine => ornithine + guanidoacetate (Homo sapiens)
GATM dimer [mitochondrial intermembrane space] (Homo sapiens)
GATM [mitochondrial intermembrane space] (Homo sapiens)
External Reference Information
External Reference
UniProt:P50440 GATM
Gene Names
GATM, AGAT
Chain
transit peptide:1-43, chain:44-423
Reference Genes
BioGPS Gene:2628 GATM
COSMIC (genes):GATM GATM
CTD Gene:2628 GATM
dbSNP Gene:2628 GATM
ENSEMBL:ENSG00000171766 GATM
HGNC:4175 GATM
KEGG:hsa:2628 GATM
Monarch:2628 GATM
NCBI Gene:2628 GATM
OMIM:602360 GATM
UCSC:P50440 GATM
Reference Transcript
RefSeq:NM_001482.2 GATM
Other Identifiers
11716813_a_at
11716814_s_at
11746069_a_at
1557692_PM_a_at
1557692_a_at
1566861_PM_at
1566861_at
16808665
203178_PM_at
203178_at
216733_PM_s_at
216733_s_at
2628
3622389
3622390
3622391
3622392
3622393
3622394
3622395
3622396
3622397
3622398
3622399
3622400
3622401
3622402
3622403
3622404
3622405
3622406
3622407
3622408
3622409
3622410
3622411
3622412
3622413
36595_s_at
36596_r_at
55135_at
7988414
A_23_P129064
GE58793
GO:0003012
GO:0003824
GO:0005515
GO:0005737
GO:0005739
GO:0005743
GO:0005758
GO:0006575
GO:0006600
GO:0006601
GO:0007611
GO:0014889
GO:0015067
GO:0015068
GO:0016740
GO:0043226
GO:0050877
GO:0070062
GO:0120162
HMNXSV003021512
HMNXSV003040737
HMNXSV003044854
Hs.75335.3.S1_3p_a_at
Hs2.155294.1.S1_3p_s_at
Hs2.155294.2.S1_3p_at
ILMN_1729180
PH_hs_0040412
S68805_at
TC15002518.hg
TC15002814.hg
TC15002815.hg
X86401_s_at
g4503932_3p_at
p5141
p5142
Participates
as a component of
GATM dimer [mitochondrial intermembrane space] (Homo sapiens)
Inferred To
gatm [mitochondrial intermembrane space]
(Danio rerio)
gatm [mitochondrial intermembrane space]
(Xenopus tropicalis)
GATM [mitochondrial intermembrane space]
(Bos taurus)
GATM [mitochondrial intermembrane space]
(Canis familiaris)
GATM [mitochondrial intermembrane space]
(Gallus gallus)
GATM [mitochondrial intermembrane space]
(Mus musculus)
GATM [mitochondrial intermembrane space]
(Rattus norvegicus)
GATM [mitochondrial intermembrane space]
(Sus scrofa)
Cross References
Guide to Pharmacology - Targets
1246
ENSEMBL
ENSP00000502445
,
ENST00000558336
,
ENST00000675323
,
ENSP00000454008
,
ENSP00000379895
,
ENST00000396659
OpenTargets
ENSG00000171766
IntEnz
2.1.4.1
HPA
ENSG00000171766-GATM
PRO
P50440
Pharos - Targets
P50440
Orphanet
GATM
HMDB Protein
HMDBP00463
PDB
2JDX
,
2JDW
,
6JDW
,
1JDW
,
1JDX
,
7JDW
,
3JDW
,
8JDW
,
9JDW
,
4JDW
,
5JDW
Interactors (4)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q9P1W8 SIRPG
1
SIRPG [plasma membrane]
(R-HSA-197571)
0.556
3
UniProt:Q14693 LPIN1
3
LPIN1 [endoplasmic reticulum membrane]
(R-HSA-549157)
LPIN1 [nuclear envelope]
(R-HSA-4419927)
p-S106-LPIN1 [nucleoplasm]
(R-HSA-4419936)
0.556
3
UniProt:Q13352 ITGB3BP
2
ITGB3BP [nucleoplasm]
(R-HSA-606325)
ITGB3BP [cytosol]
(R-HSA-3006405)
0.556
3
UniProt:Q14457 BECN1
4
BECN1 [cytosol]
(R-HSA-1632841)
p-S15-BECN1 [cytosol]
(R-HSA-5682391)
ISG15-K-BECN1 [cytosol]
(R-HSA-9853030)
K63polyUb-BECN1 [cytosol]
(R-HSA-6782989)
0.556
3
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