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HADH [mitochondrial matrix]
Stable Identifier
R-HSA-71051
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
short chain 3-hydroxyacyl-CoA dehydrogenase monomer, HCDH_HUMAN, Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial precursor , HCDH, Medium and short chain L-3-hydroxyacyl-coenzyme A dehydrogenase
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Homo sapiens)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Homo sapiens)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Homo sapiens)
HADH dimer [mitochondrial matrix] (Homo sapiens)
HADH [mitochondrial matrix] (Homo sapiens)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Homo sapiens)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Homo sapiens)
HADH dimer [mitochondrial matrix] (Homo sapiens)
HADH [mitochondrial matrix] (Homo sapiens)
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Homo sapiens)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Homo sapiens)
HADH dimer [mitochondrial matrix] (Homo sapiens)
HADH [mitochondrial matrix] (Homo sapiens)
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Homo sapiens)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Homo sapiens)
HADH dimer [mitochondrial matrix] (Homo sapiens)
HADH [mitochondrial matrix] (Homo sapiens)
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Homo sapiens)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Homo sapiens)
HADH dimer [mitochondrial matrix] (Homo sapiens)
HADH [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q16836 HADH
Gene Names
HADH, HAD, HAD1, HADHSC, SCHAD
Chain
transit peptide:1-12, chain:13-314
Reference Genes
BioGPS Gene:3033 HADH
COSMIC (genes):HADH HADH
CTD Gene:3033 HADH
dbSNP Gene:3033 HADH
ENSEMBL:ENSG00000138796.18 HADH
HGNC:4799 HADH
KEGG Gene (Homo sapiens):3033 HADH
Monarch:3033 HADH
NCBI Gene:3033 HADH
OMIM:601609 HADH
UCSC:Q16836 HADH
Reference Transcript
RefSeq:NM_001184705.2 HADH
RefSeq:NM_005327.4 HADH
Other Identifiers
0002650092
11722555_s_at
11750103_a_at
16969591
201035_PM_s_at
201035_s_at
201036_PM_s_at
201036_s_at
211569_PM_s_at
211569_s_at
2738724
2738725
2738726
2738741
2738742
2738743
2738744
2738746
2738752
2738755
2738756
2738757
2738758
3033
35435_s_at
38768_at
8096753
A_23_P167227
GE61907
GO:0003857
GO:0005622
GO:0005634
GO:0005654
GO:0005737
GO:0005739
GO:0005759
GO:0006629
GO:0006631
GO:0006635
GO:0009410
GO:0009725
GO:0014823
GO:0016491
GO:0016616
GO:0016740
GO:0023052
GO:0032868
GO:0042802
GO:0043226
GO:0046676
GO:0050796
GO:0070403
GO:0120162
HMNXSV003051807
ILMN_1719906
PH_hs_0000868
PH_hs_0030960
TC04000556.hg
X96752_at
g12653080_3p_s_at
g2078328_3p_a_at
Participates
as a component of
HADH dimer [mitochondrial matrix] (Homo sapiens)
Inferred To
HADH [mitochondrial matrix]
(Bos taurus)
HADH [mitochondrial matrix]
(Caenorhabditis elegans)
HADH [mitochondrial matrix]
(Canis familiaris)
HADH [mitochondrial matrix]
(Danio rerio)
HADH [mitochondrial matrix]
(Gallus gallus)
HADH [mitochondrial matrix]
(Mus musculus)
HADH [mitochondrial matrix]
(Rattus norvegicus)
HADH [mitochondrial matrix]
(Sus scrofa)
HADH [mitochondrial matrix]
(Xenopus tropicalis)
Homologues of HADH [mitochondrial matrix]
(Bos taurus)
Cross References
RefSeq
NP_005318.3
,
NP_001171634.2
OpenTargets
ENSG00000138796
GeneCards
Q16836
HPA
ENSG00000138796-HADH
Ensembl
ENSP00000474560
,
ENST00000603302
,
ENSP00000312288
,
ENSG00000138796
,
ENST00000309522
PRO
Q16836
Pharos - Targets
Q16836
Orphanet
16181
HMDB Protein
HMDBP00381
PDB
1LSJ
,
2HDH
,
1F0Y
,
1LSO
,
1M76
,
1F17
,
1IL0
,
1M75
,
1F14
,
3RQS
,
1F12
,
3HAD
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