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ACAD8 [mitochondrial matrix]
Stable Identifier
R-HSA-70855
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
isobutyryl-CoA dehydrogenase, acyl-CoA dehydrogenase family member 8, Acyl-CoA dehydrogenase family member 8, mitochondrial precursor , Activator- recruited cofactor 42 kDa component, ARC42
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Homo sapiens)
ACAD8 tetramer [mitochondrial matrix] (Homo sapiens)
ACAD8 [mitochondrial matrix] (Homo sapiens)
Literature References
PubMed ID
Title
Journal
Year
14752098
Structures of isobutyryl-CoA dehydrogenase and enzyme-product complex: comparison with isovaleryl- and short-chain acyl-CoA dehydrogenases
Kim, JJ
,
Battaile, KP
,
Vockley, J
,
Nguyen, TV
J Biol Chem
2004
External Reference Information
External Reference
UniProt:Q9UKU7 ACAD8
Gene Names
ACAD8, ARC42, IBD
Chain
transit peptide:1-22, chain:23-415
Reference Genes
BioGPS Gene:27034 ACAD8
COSMIC (genes):ACAD8 ACAD8
CTD Gene:27034 ACAD8
dbSNP Gene:27034 ACAD8
ENSEMBL:ENSG00000151498 ACAD8
HGNC:87 ACAD8
KEGG Gene (Homo sapiens):27034 ACAD8
Monarch:27034 ACAD8
NCBI Gene:27034 ACAD8
OMIM:604773 ACAD8
UCSC:Q9UKU7 ACAD8
Reference Transcript
RefSeq:NM_014384.2 ACAD8
Other Identifiers
0002320242
11746914_a_at
11746915_x_at
11747492_a_at
11754333_a_at
221669_PM_s_at
221669_s_at
27034
3357304
3357305
3357309
3357310
3357312
3357314
3357316
3357326
3357327
3357328
3357331
3357338
3357339
63383_at
7945283
A_24_P4678
GE58588
GO:0003674
GO:0003995
GO:0005575
GO:0005622
GO:0005737
GO:0005739
GO:0005759
GO:0006520
GO:0006574
GO:0006629
GO:0008150
GO:0009056
GO:0009083
GO:0016491
GO:0016627
GO:0043167
GO:0043226
GO:0044281
GO:0050660
HMNXSV003023126
ILMN_2225595
PH_hs_0001397
TC11001215.hg
g12805020_3p_a_at
Participates
as a component of
ACAD8 tetramer [mitochondrial matrix] (Homo sapiens)
Inferred To
ACAD8 [mitochondrial matrix]
(Bos taurus)
ACAD8 [mitochondrial matrix]
(Canis familiaris)
ACAD8 [mitochondrial matrix]
(Gallus gallus)
acdh-9 [mitochondrial matrix]
(Caenorhabditis elegans)
Acad8 [mitochondrial matrix]
(Mus musculus)
Acad8 [mitochondrial matrix]
(Rattus norvegicus)
acad8 [mitochondrial matrix]
(Danio rerio)
acad8 [mitochondrial matrix]
(Dictyostelium discoideum)
acad8 [mitochondrial matrix]
(Xenopus tropicalis)
Cross References
RefSeq
NP_055199.1
OpenTargets
ENSG00000151498
HPA
ENSG00000151498-ACAD8
GeneCards
Q9UKU7
Ensembl
ENSG00000151498
,
ENST00000281182
,
ENSP00000363884
,
ENSP00000281182
,
ENST00000374752
PRO
Q9UKU7
Pharos - Targets
Q9UKU7
Orphanet
16425
PDB
1RX0
HMDB Protein
HMDBP05273
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