Mitochondrial ornithine transcarbamoylase (OTC) catalyzes the reaction of ornithine and carbamoyl phosphate to form citrulline (Horwich et al. 1984). The enzyme is a homotrimer (Shi et al. 2001).
Shi, D, Morizono, H, Yu, X, Tong, L, Allewell, NM, Tuchman, M
Horwich, AL, Fenton, WA, Williams, KR, Kalousek, F, Kraus, JP, Doolittle, RF, Konigsberg, W, Rosenberg, LE
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