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aKADH E3 dimer [mitochondrial matrix]
Stable Identifier
R-HSA-69980
Type
Complex
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
alpha-keto acid dehydrogenase E3 homodimer
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
BCKDH transfers CoA group from CoA-SH to BCAAs (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
BCKDK phosphorylates BCKDH (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
p-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
PPM1K dephosphorylates p-BCKDH (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
p-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
Glyoxylate metabolism and glycine degradation (Homo sapiens)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Homo sapiens)
DHs [mitochondrial matrix] (Homo sapiens)
BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
lipoylated DHs [mitochondrial matrix] (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
lipo-aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
Lysine catabolism (Homo sapiens)
alpha-ketoadipate + CoASH + NAD+ => glutaryl-CoA + CO2 + NADH + H+ (Homo sapiens)
lipo-aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Pyruvate metabolism and Citric Acid (TCA) cycle (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
alpha-ketoglutarate + CoASH + NAD+ => succinyl-CoA + CO2 + NADH + H+ (Homo sapiens)
lipo-aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
Pyruvate metabolism (Homo sapiens)
Regulation of pyruvate dehydrogenase (PDH) complex (Homo sapiens)
PDK isoforms phosphorylate lipo-PDH (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
p-lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
PDP dephosphorylates p-lipo-PDH (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
p-lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
lipo-PDH decarboxylates PYR to Ac-CoA (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
Signal Transduction (Homo sapiens)
Signaling by Nuclear Receptors (Homo sapiens)
Signaling by Retinoic Acid (Homo sapiens)
PDK isoforms phosphorylate lipo-PDH (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
p-lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
Participants
components
x 2
aKADH E3 [mitochondrial matrix]
(Homo sapiens)
Participates
as a component of
PDH [mitochondrial matrix] (Homo sapiens)
aKGDH [mitochondrial matrix] (Homo sapiens)
BCKDH [mitochondrial matrix] (Homo sapiens)
p-BCKDH [mitochondrial matrix] (Homo sapiens)
p-lipo-PDH [mitochondrial matrix] (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
lipo-aKGDH [mitochondrial matrix] (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
Inferred To
aKADH E3 dimer [mitochondrial matrix]
(Bos taurus)
aKADH E3 dimer [mitochondrial matrix]
(Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix]
(Canis familiaris)
aKADH E3 dimer [mitochondrial matrix]
(Danio rerio)
aKADH E3 dimer [mitochondrial matrix]
(Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix]
(Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix]
(Gallus gallus)
aKADH E3 dimer [mitochondrial matrix]
(Mus musculus)
aKADH E3 dimer [mitochondrial matrix]
(Plasmodium falciparum)
aKADH E3 dimer [mitochondrial matrix]
(Rattus norvegicus)
aKADH E3 dimer [mitochondrial matrix]
(Saccharomyces cerevisiae)
aKADH E3 dimer [mitochondrial matrix]
(Schizosaccharomyces pombe)
aKADH E3 dimer [mitochondrial matrix]
(Sus scrofa)
aKADH E3 dimer [mitochondrial matrix]
(Xenopus tropicalis)
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