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MT-ND3 [mitochondrial inner membrane]
Stable Identifier
R-HSA-60557
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase chain 3 (EC 1.6.5.3)
Icon
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
COA1:MT-ND2, TMEM186:MT-ND3, MT-ND6, NDUFB6 bind the MCIA complex to form a 370kDa subcomplex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane] (Homo sapiens)
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:P03897 MT-ND3
Gene Names
MT-ND3, MTND3, NADH3, ND3
Chain
chain:1-115
Reference Genes
BioGPS Gene:4537 MT-ND3
COSMIC (genes):MT-ND3 MT-ND3
CTD Gene:4537 MT-ND3
dbSNP Gene:4537 MT-ND3
ENSEMBL:ENSG00000198840 MT-ND3
ENSEMBL_homo_sapiens_GENE:ENSG00000198840.2 MT-ND3
HGNC:7458 MT-ND3
KEGG Gene (Homo sapiens):4537 MT-ND3
Monarch:4537 MT-ND3
NCBI Gene:4537 MT-ND3
OMIM:516002 MT-ND3
Reference Transcript
RefSeq:NC_012920.1 MT-ND3
Other Identifiers
11764256_s_at
1553588_PM_at
1553588_at
17100667
17100669
17100671
17100673
17100675
17100677
17100679
17119762
17126270
17126272
17126278
224372_PM_at
224372_at
224373_PM_s_at
224373_s_at
4037648
4037649
4037651
4037653
4037655
4037657
4037658
4037659
4037660
4037661
4037662
4037664
4037666
4037668
4537
8165672
8165674
8165676
8165680
8165682
8165684
A_23_P315252
A_23_P360209
A_33_P3336696
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0006979
GO:0008137
GO:0009060
GO:0009642
GO:0009725
GO:0016020
GO:0016491
GO:0022900
GO:0031966
GO:0042776
GO:0043226
GO:0055086
GO:0070469
GO:0071385
GO:1901135
HMNXSV003008622
HMNXSV003015713
Hs2Affx.1.52.S1_3p_at
RNA143452|tRNA_369_71
RNA143502|tRNA_419_69
TC08001295.hg
TC0M000006.hg
TC0M000007.hg
TC0M000008.hg
TC0M000023.hg
g12005804_3p_at
p28385
Participates
as a component of
TMEM186:MT-ND3 [mitochondrial inner membrane] (Homo sapiens)
Inferred To
mt-nd3 [mitochondrial inner membrane]
(Danio rerio)
mt-nd3 [mitochondrial inner membrane]
(Xenopus tropicalis)
nduo-3 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Ghost homologue of MT-ND3 [mitochondrial inner membrane]
(Canis familiaris)
mt-Nd3 [mitochondrial inner membrane]
(Mus musculus)
mt-Nd3 [mitochondrial inner membrane]
(Rattus norvegicus)
mt:ND3 [mitochondrial inner membrane]
(Drosophila melanogaster)
MT-ND3 [mitochondrial inner membrane]
(Bos taurus)
MT-ND3 [mitochondrial inner membrane]
(Gallus gallus)
MT-ND3 [mitochondrial inner membrane]
(Sus scrofa)
Cross References
RefSeq
YP_003024033.1
OpenTargets
ENSG00000198840
IntEnz
7.1.1.2
HPA
ENSG00000198840-MT-ND3
GeneCards
P03897
Ensembl
ENSG00000198840
,
ENST00000361227
,
ENSP00000355206
PRO
P03897
Pharos - Targets
P03897
Orphanet
16480
HMDB Protein
HMDBP00182
PDB
5XTC
,
5XTD
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