Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
ACSF3 [mitochondrial matrix]
Stable Identifier
R-HSA-5696011
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Acyl-CoA synthetase family member 3, mitochondrial ecNumber6.2.1.-/ecNumber, ACSF3_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Fatty acyl-CoA biosynthesis (Homo sapiens)
Synthesis of very long-chain fatty acyl-CoAs (Homo sapiens)
ACSF3 ligates CoA-SH to VLCFA (Homo sapiens)
ACSF3 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q4G176 ACSF3
Gene Names
ACSF3, PSEC0197
Chain
transit peptide:1-83, chain:84-576
Reference Genes
BioGPS Gene:197322 ACSF3
COSMIC (genes):ACSF3 ACSF3
CTD Gene:197322 ACSF3
dbSNP Gene:197322 ACSF3
ENSEMBL:ENSG00000176715 ACSF3
HGNC:27288 ACSF3
KEGG:hsa:197322 ACSF3
Monarch:197322 ACSF3
NCBI Gene:197322 ACSF3
OMIM:614245 ACSF3
UCSC:Q4G176 ACSF3
Reference Transcript
RefSeq:NM_001243279.2 ACSF3
RefSeq:NM_174917.4 ACSF3
RefSeq:NM_001127214.3 ACSF3
Other Identifiers
11734838_a_at
11754897_a_at
1553450_PM_s_at
1553450_s_at
1556552_PM_a_at
1556552_a_at
1564334_PM_at
1564334_at
16821894
16821919
16821924
197322
227464_PM_at
227464_at
235823_PM_at
235823_at
3673824
3673825
3673828
3673829
3673830
3673831
3673832
3673833
3673836
3673840
3673841
3673844
3673845
3673846
3673847
3673849
3673850
3673851
3673856
3673857
3673858
3673859
3673860
3673861
3673862
3673863
3673864
3673865
3673866
3673867
3673868
3673869
3673870
3673871
3673881
3673887
3673889
3673890
3673891
46000_r_at
57597_at
76242_at
7997863
A_14_P112567
A_14_P117818
A_14_P124841
A_14_P136006
A_23_P401024
A_24_P239309
A_32_P218332
GE87809
GO:0000166
GO:0003824
GO:0005515
GO:0005524
GO:0005654
GO:0005739
GO:0005759
GO:0006629
GO:0006631
GO:0006633
GO:0006790
GO:0016874
GO:0016878
GO:0031957
GO:0035338
GO:0043226
GO:0055086
GO:0090409
GO:0090410
GO:0140657
GO:1901135
HMNXSV003040375
HMNXSV003045074
Hs.120155.0.A1_3p_at
Hs.269783.0.A1_3p_at
Hs.269783.0.A1_3p_x_at
Hs2.123661.1.S1_3p_a_at
Hs2.375664.1.S1_3p_at
Hs2.376413.1.S1_3p_s_at
ILMN_1716832
ILMN_1722825
PH_hs_0018248
PH_hs_0025382
PH_hs_0038615
TC16000689.hg
TC16000691.hg
TC16001704.hg
TC16001705.hg
p6599
p6600
Inferred To
ACSF3 [mitochondrial matrix]
(Bos taurus)
ACSF3 [mitochondrial matrix]
(Dictyostelium discoideum)
ACSF3 [mitochondrial matrix]
(Mus musculus)
ACSF3 [mitochondrial matrix]
(Sus scrofa)
Acsf3 [mitochondrial matrix]
(Drosophila melanogaster)
Acsf3 [mitochondrial matrix]
(Rattus norvegicus)
Cross References
ENSEMBL
ENST00000614302
,
ENST00000406948
,
ENSP00000479130
,
ENSP00000320646
,
ENSP00000384627
,
ENST00000317447
OpenTargets
ENSG00000176715
HPA
ENSG00000176715-ACSF3
PRO
Q4G176
Pharos - Targets
Q4G176
GlyGen
Q4G176
Orphanet
ACSF3
HMDB Protein
HMDBP10999
Interactors (12)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P10809 HSPD1
6
HSPD1(1-573) [cytosol]
(R-HSA-1267989)
HSPD1(1-573) [mitochondrial intermembrane space]
(R-HSA-1267963)
HSPD1(1-26) [mitochondrial matrix]
(R-HSA-8986171)
HSPD1(1-573) [mitochondrial inner membrane]
(R-HSA-1299442)
HSPD1 [mitochondrial inner membrane]
(R-HSA-1299455)
HSPD1 [mitochondrial matrix]
(R-HSA-1299448)
0.615
5
UniProt:Q9BQ13 KCD14
0.564
2
UniProt:Q6A162 KRT40
1
KRT40 [cytosol]
(R-HSA-6809605)
0.556
3
UniProt:P51157 RAB28
0.556
3
UniProt:P14373 TRIM27
2
TRIM27 [cytosol]
(R-HSA-8851002)
TRIM27 [nucleoplasm]
(R-HSA-2997690)
0.556
3
UniProt:Q96KQ4 PPP1R13B
1
PPP1R13B [nucleoplasm]
(R-HSA-6799775)
0.556
3
UniProt:O95460-2 MATN4
0.556
3
UniProt:O75251 NDUFS7
1
NDUFS7 [mitochondrial matrix]
(R-HSA-6788521)
0.527
3
UniProt:Q9BVS5 TRMT61B
1
TRMT61B [mitochondrial matrix]
(R-HSA-6787512)
0.527
2
UniProt:Q6ZMB5 T184A
0.527
2
UniProt:P21912 SDHB
2
SDHB [mitochondrial inner membrane]
(R-HSA-70985)
SDHB [mitochondrial matrix]
(R-HSA-9854983)
0.527
2
UniProt:Q5BKU9 OXLD1
0.527
2
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text