XPC is mutated in individuals with xeroderma pigmentosum from genetic Complementation Group C (XP-C). It forms a tight complex with RAD23B (HR23B) or, to a lesser extent, RAD23A (HR23A), two human homologs of yeast Rad23 (Masutani et al. 1994, Ng et al. 2003). CETN2 (centrin 2, CEN2) is also part of the XPC complex with RAD23 (Araki et al. 2001, Nishi et al. 2005).
Kondoh, J, Takemura, M, Uchida, A, Masutani, C, Sugasawa, K, Hanaoka, F, Ohkuma, Y, Araki, M
Okuda, Y, Mori, T, Watanabe, E, Iwai, S, Sugasawa, K, Hanaoka, F, Nishi, R, Masutani, C
Takio, K, Bootsma, D, van der Spek, PJ, Enomoto, T, Sonoyama, T, Masutani, C, Ui, M, Yanagisawa, J, Sugasawa, K, Tanaka, K
Sugasawa, K, Bergink, S, Ng, JM, van der Horst, GT, Vrieling, H, Hoeijmakers, JH, Vermeulen, W
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