Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
PPT1 [lysosomal lumen]
Stable Identifier
R-HSA-5690068
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
lysosomal lumen
Synonyms
Palmitoyl-protein thioesterase 1, PPT1_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Fatty acyl-CoA biosynthesis (Homo sapiens)
PPT1 hydrolyses palmitoylated proteins (Homo sapiens)
PPT1 [lysosomal lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:P50897 PPT1
Gene Names
PPT1, CLN1, PPT
Chain
signal peptide:1-27, chain:28-306
Reference Genes
BioGPS Gene:5538 PPT1
COSMIC (genes):PPT1 PPT1
CTD Gene:5538 PPT1
dbSNP Gene:5538 PPT1
ENSEMBL:ENSG00000131238 PPT1
HGNC:9325 PPT1
KEGG:hsa:5538 PPT1
Monarch:5538 PPT1
NCBI Gene:5538 PPT1
OMIM:600722 PPT1
UCSC:P50897 PPT1
Reference Transcript
RefSeq:NM_000310.3 PPT1
RefSeq:NM_001142604.1 PPT1
Other Identifiers
11716533_a_at
11716534_s_at
11716535_a_at
11742107_a_at
11742108_a_at
11756724_x_at
16685779
200975_PM_at
200975_at
2408190
2408191
2408192
2408193
2408194
2408195
2408196
2408197
2408198
2408199
2408200
2408201
2408202
34774_at
5538
7915286
A_23_P62659
A_24_P276628
GE59177
GO:0002084
GO:0003824
GO:0005515
GO:0005576
GO:0005615
GO:0005634
GO:0005764
GO:0005765
GO:0005773
GO:0005794
GO:0005829
GO:0006629
GO:0006790
GO:0006898
GO:0006907
GO:0007040
GO:0007042
GO:0007269
GO:0007399
GO:0007420
GO:0007601
GO:0007625
GO:0008021
GO:0008289
GO:0008306
GO:0008344
GO:0008474
GO:0009057
GO:0015031
GO:0016020
GO:0016042
GO:0016192
GO:0016787
GO:0030149
GO:0030163
GO:0030308
GO:0030424
GO:0030425
GO:0030672
GO:0031410
GO:0031579
GO:0034164
GO:0035727
GO:0043025
GO:0043066
GO:0043202
GO:0043226
GO:0043231
GO:0043524
GO:0045121
GO:0046949
GO:0048260
GO:0048549
GO:0048666
GO:0048856
GO:0050803
GO:0050877
GO:0052816
GO:0055086
GO:0061024
GO:0070062
GO:0098599
GO:0098734
GO:0099523
GO:0120146
GO:0140096
GO:1901135
HMNXSV003015266
HMNXSV003033642
ILMN_1669273
PH_hs_0030902
TC01002553.hg
U44772_at
g4506030_3p_at
Inferred To
Ppt1 [lysosomal lumen]
(Drosophila melanogaster)
Ppt1 [lysosomal lumen]
(Mus musculus)
Ppt1 [lysosomal lumen]
(Rattus norvegicus)
ppt-1 [lysosomal lumen]
(Caenorhabditis elegans)
PPT1 [lysosomal lumen]
(Bos taurus)
PPT1 [lysosomal lumen]
(Canis familiaris)
PPT1 [lysosomal lumen]
(Gallus gallus)
PPT1 [lysosomal lumen]
(Sus scrofa)
ppt1 [lysosomal lumen]
(Danio rerio)
ppt1 [lysosomal lumen]
(Dictyostelium discoideum)
ppt1 [lysosomal lumen]
(Xenopus tropicalis)
Cross References
Guide to Pharmacology - Targets
3199
ENSEMBL
ENST00000449045
,
ENSP00000493153
,
ENST00000529905
,
ENSP00000432053
,
ENST00000642050
,
ENSP00000392293
OpenTargets
ENSG00000131238
HPA
ENSG00000131238-PPT1
ZINC - Substances
PPT1_HUMAN
ZINC target
P50897
PRO
P50897
Pharos - Targets
P50897
GlyGen
P50897
Orphanet
PPT1
HMDB Protein
HMDBP01050
PDB
3GRO
Interactors (10)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q99932-2 SPAG8
0.556
3
UniProt:Q8WXF7 ATLA1
0.556
3
UniProt:P26436 ASPX
0.556
3
UniProt:Q3KNS6-3 Q3KNS63
0.556
3
UniProt:Q6ZR37 PKHG7
0.556
3
UniProt:Q9Y575-3 ASB3
0.556
3
IntAct:EBI-25842396 CCSB
0.556
3
UniProt:O75925 PIAS1
1
PIAS1 [nucleoplasm]
(R-HSA-877307)
0.556
3
UniProt:A0A663DJA2 ORF10
0.527
2
UniProt:Q76RH3 Q76RH3
0.499
2
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text