Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
JOSD1 [cytosol]
Stable Identifier
R-HSA-5688784
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
cytosol
Synonyms
Josephin-1 ecNumber3.4.19.12/ecNumber, JOS1_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Deubiquitination (Homo sapiens)
Josephin domain DUBs (Homo sapiens)
ATXN3 family cleave Ub chains (Homo sapiens)
ATXN3,ATXN3L,JOSD1,JOSD2 [cytosol] (Homo sapiens)
JOSD1 [cytosol] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q15040 JOSD1
Gene Names
JOSD1, JSPH1, KIAA0063
Chain
chain:1-202
Reference Genes
BioGPS Gene:9929 JOSD1
COSMIC (genes):JOSD1 JOSD1
CTD Gene:9929 JOSD1
dbSNP Gene:9929 JOSD1
ENSEMBL:ENSG00000100221 JOSD1
HGNC:28953 JOSD1
Monarch:9929 JOSD1
NCBI Gene:9929 JOSD1
OMIM:615323 JOSD1
UCSC:Q15040 JOSD1
Reference Transcript
RefSeq:XM_005261879.2 JOSD1
RefSeq:XM_005261878.2 JOSD1
RefSeq:XM_005261876.2 JOSD1
RefSeq:NM_014876.5 JOSD1
RefSeq:XM_005261877.2 JOSD1
Other Identifiers
11719494_at
11755160_a_at
16935130
201751_PM_at
201751_at
229076_PM_s_at
229076_s_at
239912_PM_at
239912_at
34333_at
3960779
3960781
3960783
3960784
3960785
3960786
3960787
3960788
3960789
3960793
3960794
3960795
3960796
3960797
3960798
3960799
3960800
3960801
3960803
3960804
3960805
3960807
8076128
89308_at
9929
A_23_P6474
A_24_P271527
A_32_P82963
D31884_at
GE57168
GO:0003824
GO:0004843
GO:0005515
GO:0005737
GO:0005829
GO:0005886
GO:0006508
GO:0008233
GO:0016020
GO:0016579
GO:0016787
GO:0140096
HMNXSV003054860
Hs.181654.0.A1_3p_at
Hs.285005.1.A1_3p_x_at
ILMN_1668535
PH_hs_0000386
TC22000796.hg
g7661887_3p_at
Participates
as a member of
ATXN3,ATXN3L,JOSD1,JOSD2 [cytosol] (Homo sapiens)
Inferred To
josd1 [cytosol]
(Danio rerio)
josd1 [cytosol]
(Xenopus tropicalis)
Josd [cytosol]
(Drosophila melanogaster)
josd-1 [cytosol]
(Caenorhabditis elegans)
Josd1 [cytosol]
(Mus musculus)
Josd1 [cytosol]
(Rattus norvegicus)
JOSD1 [cytosol]
(Canis familiaris)
JOSD1 [cytosol]
(Dictyostelium discoideum)
JOSD1 [cytosol]
(Gallus gallus)
JOSD1 [cytosol]
(Plasmodium falciparum)
JOSD1 [cytosol]
(Sus scrofa)
Cross References
ENSEMBL
ENSP00000506752
,
ENST00000216039
,
ENST00000683374
,
ENSP00000216039
OpenTargets
ENSG00000100221
HPA
ENSG00000100221-JOSD1
PRO
Q15040
Pharos - Targets
Q15040
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P14373 TRIM27
2
TRIM27 [cytosol]
(R-HSA-8851002)
TRIM27 [nucleoplasm]
(R-HSA-2997690)
0.666
4
UniProt:Q7Z3S9 NOTCH2NLA
3
NOTCH2NLA [extracellular region]
(R-HSA-9908935)
NOTCH2NLA(1-?) [extracellular region]
(R-HSA-9911493)
NOTCH2NLA(?-236) [extracellular region]
(R-HSA-9911490)
0.556
3
UniProt:Q13077 TRAF1
3
TRAF1 [cytosol]
(R-HSA-5634163)
TRAF1(1-163) [cytosol]
(R-HSA-5634199)
TRAF1(164-416) [cytosol]
(R-HSA-5634204)
0.556
3
UniProt:P0DPK4 NOTCH2NLC
1
NOTCH2NLC [extracellular region]
(R-HSA-9908932)
0.556
3
UniProt:P22735 TGM1
3
TGM1 [cytosol]
(R-HSA-6813756)
TGM1 [cornified envelope]
(R-HSA-8847706)
TGM1 [plasma membrane]
(R-HSA-6813757)
0.556
3
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text