Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
RibC-GLUD1 [mitochondrial matrix]
Stable Identifier
R-HSA-5688244
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Glutamate dehydrogenase 1, mitochondrial precursor
Locations in the PathwayBrowser
Expand all
Organelle biogenesis and maintenance (Homo sapiens)
Mitochondrial biogenesis (Homo sapiens)
Transcriptional activation of mitochondrial biogenesis (Homo sapiens)
SIRT4 transfers ADPRib to GLUD (Homo sapiens)
RibC-GLUD [mitochondrial matrix] (Homo sapiens)
RibC-GLUD1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P00367 GLUD1
Gene Names
GLUD1, GLUD
Chain
transit peptide:1-53, chain:54-558
Reference Genes
BioGPS Gene:2746 GLUD1
COSMIC (genes):GLUD1 GLUD1
CTD Gene:2746 GLUD1
dbSNP Gene:2746 GLUD1
ENSEMBL:ENSG00000148672 GLUD1
HGNC:4335 GLUD1
KEGG:hsa:2746 GLUD1
Monarch:2746 GLUD1
NCBI Gene:2746 GLUD1
OMIM:138130 GLUD1
UCSC:P00367 GLUD1
Reference Transcript
RefSeq:NM_001318905.1 GLUD1
RefSeq:NM_005271.4 GLUD1
RefSeq:NM_001318902.1 GLUD1
RefSeq:NM_001318901.1 GLUD1
RefSeq:NM_001318904.1 GLUD1
RefSeq:NM_001318906.1 GLUD1
RefSeq:NM_001318900.1 GLUD1
Other Identifiers
11716206_a_at
11716207_s_at
11716208_s_at
11750168_x_at
16716239
200946_PM_x_at
200946_x_at
200947_PM_s_at
200947_s_at
215794_PM_x_at
215794_x_at
2746
31691_g_at
3244899
3244901
3244940
3245599
3245600
3245601
3251816
3251817
3251843
3298976
3298978
3298979
3298980
3298981
3298982
3298983
3298984
3298987
3298988
3298989
3298990
3298991
3298992
3298993
3298994
3298995
3298998
3298999
3299000
3299001
3299002
3299008
3299009
3299010
3299011
3299012
3299013
3299017
3299018
3299019
3299020
3299023
3299024
3299025
3299026
3299027
3299028
37341_at
3989261
3989262
3989263
4038067
4038068
4038069
4038070
4038361
4038363
4038367
4038368
4038369
4038370
4038371
4038372
4038373
4038374
7934852
A_23_P138665
GE57862
GO:0000166
GO:0003824
GO:0004352
GO:0004353
GO:0004354
GO:0005515
GO:0005524
GO:0005525
GO:0005737
GO:0005739
GO:0005759
GO:0005783
GO:0006520
GO:0006537
GO:0006538
GO:0006541
GO:0016491
GO:0016639
GO:0021762
GO:0032024
GO:0042803
GO:0043226
GO:0043531
GO:0048856
GO:0070403
GO:0070728
GO:0072350
HMNXSV003052737
Hs.272497.1.S1_3p_s_at
Hs.77508.0.A1_3p_a_at
Hs.77508.0.A1_3p_x_at
ILMN_1713756
M20867_s_at
PH_hs_0023977
TC10001486.hg
g4885280_3p_a_at
Participates
as a member of
RibC-GLUD [mitochondrial matrix] (Homo sapiens)
Other forms of this molecule
GLUD1 [mitochondrial matrix]
Ack-GLUD1 [mitochondrial matrix]
Inferred To
Homologues of RibC-GLUD1 [mitochondrial matrix]
(Sus scrofa)
phospho-GLUD1 [mitochondrial matrix]
(Canis familiaris)
phospho-GLUD2 [mitochondrial matrix]
(Gallus gallus)
phospho-glud1b [mitochondrial matrix]
(Danio rerio)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Bos taurus)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Caenorhabditis elegans)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Dictyostelium discoideum)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Drosophila melanogaster)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Mus musculus)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Rattus norvegicus)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Sus scrofa)
phospho-RibC-GLUD1 [mitochondrial matrix]
(Xenopus tropicalis)
Modified Residues
Name
adenosine diphosphoribosyl (ADP-ribosyl) modified residue at unknown position
PsiMod Name
adenosine diphosphoribosyl (ADP-ribosyl) modified residue
PsiMod Definition
A protein modification that effectively results from forming an adduct with ADP-ribose through formation of a glycosidic bond.
Cross References
OpenTargets
ENSG00000148672
ENSEMBL
ENSP00000507316
,
ENSP00000507901
,
ENSP00000507729
,
ENST00000681988
,
ENSP00000277865
,
ENST00000682507
,
ENST00000684546
,
ENST00000277865
,
ENST00000683783
,
ENST00000683256
,
ENSP00000508098
,
ENSP00000507881
,
ENSP00000508244
,
ENSP00000508107
,
ENST00000683269
,
ENST00000684372
HPA
ENSG00000148672-GLUD1
PRO
P00367
Pharos - Targets
P00367
Orphanet
GLUD1
GlyGen
P00367
PDB
7UZM
,
1L1F
,
8SK8
,
6DQG
,
8KGY
,
1NR1
,
8W4J
HMDB Protein
HMDBP00694
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q13418 ILK
1
ILK [cytosol]
(R-HSA-432864)
0.527
2
UniProt:P13569 CFTR
17
misfolded CFTR [endoplasmic reticulum membrane]
(R-HSA-8868730)
CFTR [endoplasmic reticulum membrane]
(R-HSA-8866837)
CFTR [plasma membrane]
(R-HSA-383188)
CFTR N1303K [plasma membrane]
(R-HSA-5678983)
CFTR F508del [plasma membrane]
(R-HSA-5678978)
CFTR W1282* [plasma membrane]
(R-HSA-5678976)
CFTR G551D [plasma membrane]
(R-HSA-5678977)
CFTR G542* [plasma membrane]
(R-HSA-5678986)
ub-CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866842)
ub-CFTR F508del [cytosol]
(R-HSA-8866838)
CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866834)
PolyUb-CFTR [endosome membrane]
(R-HSA-6782976)
CFTR [endosome membrane]
(R-HSA-6782965)
CFTR [Golgi-associated vesicle membrane]
(R-HSA-5627079)
CFTR [lysosomal membrane]
(R-HSA-5627279)
PolyUb-CFTR [plasma membrane]
(R-HSA-8867595)
PolyUb-CFTR [clathrin-coated endocytic vesicle membrane]
(R-HSA-8869104)
0.483
7
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text