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MRPL13 [mitochondrial inner membrane]
Stable Identifier
R-HSA-5368244
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
39S ribosomal protein L13, mitochondrial, RM13_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Homo sapiens)
Translation (Homo sapiens)
Mitochondrial translation (Homo sapiens)
Mitochondrial ribosome-associated quality control (Homo sapiens)
55S mitochondrial ribosome:non-stop mRNA binds ICT1 (MRPL58) (Homo sapiens)
55S ribosome:non-stop mRNA:peptidyl-tRNA at P-site:tRNA at E-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:non-stop mRNA:peptidyl-tRNA at P-site:tRNA at E-site:ICT1 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
ICT1 hydrolyzes the peptidyl-tRNA bond of the nascent polypeptide (Homo sapiens)
55S ribosome:non-stop mRNA:peptidyl-tRNA at P-site:tRNA at E-site:ICT1 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:non-stop mRNA:tRNA:ICT1 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
MTRFR:MTRES1 binds 39S ribosomal subunit:mRNA:peptidyl-tRNA:tRNA:MALSU1:MIEF1:NDUFAB1 (Homo sapiens)
39S ribosomal subunit:mRNA:peptidyl-tRNA at P site:tRNA at E site:MALSU1:MIEF:NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
MTRFR:MTRES1:39S ribosomal subunit:mRNA:peptidyl-tRNA:MALSU1:MIEF1:NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit:mRNA:peptidyl-tRNA at P-site:MALSU1:MIEF1:NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
MTRFR:MTRES1:39S ribosomal subunit:mRNA:peptidyl-tRNA:MALSU1:MIEF1:NDUFAB1 dissociates (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
MTRFR:MTRES1:39S ribosomal subunit:mRNA:peptidyl-tRNA:MALSU1:MIEF1:NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit:mRNA:peptidyl-tRNA at P-site:MALSU1:MIEF1:NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
Stalled 55S mitochondrial ribosome is dissociated to yield 28S subunit and 39S subunit:mRNA:peptidyl-tRNA:tRNA (Homo sapiens)
39S ribosomal subunit:mRNA:peptidyl-tRNA at P site:tRNA at E site:MALSU1:MIEF:NDUFAB1 [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:peptidyl-tRNA at P site:tRNA at E site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
Mitochondrial translation elongation (Homo sapiens)
55S ribosome with peptidyl-tRNA in A site binds GFM1:GTP (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA at A-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA:GFM1:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
Peptide transfer from P-site to A-site (peptide bond formation) (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA at A-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
TUFM hydrolyzes GTP and TUFM:GDP dissociates from 55S ribosome (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA:TUFM:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
TUFM:GTP:aminoacyl-tRNA binds 55S ribosome:mRNA:fMet-tRNA (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA:aminoacyl-tRNA:TUFM:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
Translocation of peptidyl-tRNA from A-site to P-site (and translocation of 55S ribosome by 3 bases along mRNA) (Homo sapiens)
55S ribosome:mRNA:peptidyl-tRNA at P-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:tRNA:peptidyl-tRNA:GFM1:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
Mitochondrial translation initiation (Homo sapiens)
39S subunit binds 28S subunit:mRNA:fMet-tRNA (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:fMet-tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
Mitochondrial translation termination (Homo sapiens)
55S ribosome:MTRF1 hydrolyzes peptidyl-tRNA bond and GTP is hydrolyzed (Homo sapiens)
55S ribosome:MT-CO1,MT-ND6 mRNA:peptidyl-tRNA:tRNA:MTRF1:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:MT-CO1,MT-ND6 mRNA:tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:MTRF1L hydrolyzes peptidyl-tRNA bond and GTP is hydrolyzed (Homo sapiens)
55S ribosome:mRNA (UAA,UAG stop codon):peptidyl-tRNA:MTRF1L:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA (UAA,UAG stop codon):tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
GFM2:GTP binds 55S ribosome:mRNA:tRNA:MRRF releasing mRNA and tRNA (Homo sapiens)
55S ribosome:MRRF:GFM2:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:tRNA:MRRF [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
Hydrolysis of GTP and dissociation of 28S and 39S subunits (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:MRRF:GFM2:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
MRRF binds 55S ribosome:mRNA:tRNA (Homo sapiens)
55S ribosome:mRNA:tRNA [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA:tRNA:MRRF [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
MTRF1 and GTP bind 55S ribosome:MT-CO1,MT-ND6 mRNA:peptidyl-tRNA at P-site:tRNA at E-site (Homo sapiens)
55S ribosome:MT-CO1,MT-ND6 mRNA:peptidyl-tRNA at P-site:tRNA at E-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:MT-CO1,MT-ND6 mRNA:peptidyl-tRNA:tRNA:MTRF1:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
MTRF1L (MTRF1a) or ICT1 binds stop codon in 55S ribosome:mRNA:peptidyl-tRNA (Homo sapiens)
55S ribosome:mRNA (UAA,UAG stop codon):peptidyl-tRNA at P-site [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
55S ribosome:mRNA (UAA,UAG stop codon):peptidyl-tRNA:MTRF1L:GTP [mitochondrial inner membrane] (Homo sapiens)
55S ribosome [mitochondrial inner membrane] (Homo sapiens)
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
MRPL13 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9BYD1 MRPL13
Gene Names
MRPL13
Chain
initiator methionine:, chain:2-178
Reference Genes
BioGPS Gene:28998 MRPL13
COSMIC (genes):MRPL13 MRPL13
CTD Gene:28998 MRPL13
dbSNP Gene:28998 MRPL13
ENSEMBL:ENSG00000172172 MRPL13
HGNC:14278 MRPL13
KEGG:hsa:28998 MRPL13
Monarch:28998 MRPL13
NCBI Gene:28998 MRPL13
OMIM:610200 MRPL13
UCSC:Q9BYD1 MRPL13
Reference Transcript
RefSeq:NM_014078.5 MRPL13
Other Identifiers
11715771_a_at
11715772_x_at
17080614
218049_3p_s_at
218049_PM_s_at
218049_s_at
28998
3150799
3150800
3150801
3150802
3150803
3150804
3150805
3150810
3150811
3150812
3150813
3150816
3150819
3150821
3150822
3150824
3150825
3150826
45783_at
8152597
A_23_P44974
GE58553
GO:0003723
GO:0003729
GO:0003735
GO:0005198
GO:0005515
GO:0005739
GO:0005743
GO:0005761
GO:0005762
GO:0005840
GO:0006412
GO:0017148
GO:0032543
GO:0043226
GO:1990904
HMNXSV003023975
ILMN_1671158
PH_hs_0016363
TC08001564.hg
g7662495_3p_s_at
Participates
as a component of
39S ribosomal subunit [mitochondrial inner membrane] (Homo sapiens)
Inferred To
MRPL13 [mitochondrial inner membrane]
(Bos taurus)
MRPL13 [mitochondrial inner membrane]
(Canis familiaris)
MRPL13 [mitochondrial inner membrane]
(Gallus gallus)
MRPL13 [mitochondrial inner membrane]
(Sus scrofa)
mRpL13 [mitochondrial inner membrane]
(Drosophila melanogaster)
mrpl13 [mitochondrial inner membrane]
(Danio rerio)
mrpl-13 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Mrpl13 [mitochondrial inner membrane]
(Mus musculus)
Mrpl13 [mitochondrial inner membrane]
(Rattus norvegicus)
Cross References
RefSeq
NP_054797.2
OpenTargets
ENSG00000172172
ENSEMBL
ENST00000306185
,
ENSP00000306548
,
ENSG00000172172
HPA
ENSG00000172172-MRPL13
GeneCards
MRPL13
PRO
Q9BYD1
Pharos - Targets
Q9BYD1
GlyGen
Q9BYD1
PDB
7OG4
,
8OIT
,
7ODT
,
8XT2
,
7QH6
,
6NU2
,
8K2B
,
5OOL
,
7O9K
,
7OIC
,
7OIA
,
7OI8
,
7OI7
,
7A5H
,
7A5K
,
6ZSB
,
6ZS9
,
8OIR
,
8QU1
,
6ZSD
,
6ZSG
,
6ZSE
,
7QI5
,
6I9R
,
7QI4
,
6ZM6
,
7PD3
,
8XT3
,
8QSJ
,
7OF3
,
7OF5
,
8QU5
,
6VLZ
,
7A5I
,
7OF0
,
6VMI
,
7L20
,
7OI9
,
7ODR
,
8XT0
,
7O9M
,
7QH7
,
3J7Y
,
7PO4
,
7OIE
,
6NU3
,
7ODS
,
7A5J
,
7OI6
,
8K2A
,
7OID
,
5OOM
,
7OIB
,
6ZSA
,
6ZSC
,
7L08
,
7OF7
,
3J9M
,
7OF2
,
7OF4
,
6ZM5
,
8ANY
,
7QI6
,
7OF6
,
7A5F
,
7A5G
,
8XT1
,
8PK0
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q14197 MRPL58
2
ICT1 [mitochondrial matrix]
(R-HSA-5368175)
ICT1 [mitochondrial inner membrane]
(R-HSA-5624366)
0.643
4
UniProt:P42858 HTT
1
HTT [nucleoplasm]
(R-HSA-9023590)
0.556
3
UniProt:P62241 RPS8
2
RPS8 [cytosol]
(R-HSA-72385)
RPS8 [nucleoplasm]
(R-HSA-6791203)
0.527
3
UniProt:Q8IXZ2 ZC3H3
1
ZC3H3 [nucleoplasm]
(R-HSA-9933572)
0.527
2
UniProt:P67809 YBX1
5
p-S32,S36-YBX1 [nucleoplasm]
(R-HSA-9733227)
p-S32,S36-YBX1 [cytosol]
(R-HSA-9736837)
YBX1 [cytosol]
(R-HSA-9736840)
YBX1 [extracellular region]
(R-HSA-9017791)
YBX1 [nucleoplasm]
(R-HSA-72041)
0.527
3
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